Page last updated: 2024-08-22

acetylglucosamine and g(m2) ganglioside

acetylglucosamine has been researched along with g(m2) ganglioside in 10 studies

Research

Studies (10)

TimeframeStudies, this research(%)All Research%
pre-19903 (30.00)18.7374
1990's2 (20.00)18.2507
2000's2 (20.00)29.6817
2010's2 (20.00)24.3611
2020's1 (10.00)2.80

Authors

AuthorsStudies
Dos Santos, MR; Maia, M; Pinto, RA; Ribeiro, MG; Sá Miranda, MC1
Hirabayashi, Y; Li, SC; Li, YT1
Hinrichs, U; Kytzia, HJ; Sandhoff, K1
Hechtman, P; Kachra, Z1
Rapola, J1
Ishibashi, Y; Itakura, T; Itoh, K; Kuroki, A; Kuwahara, J; Tsuji, D; Yamanaka, S1
Cunningham, MW; Kirvan, CA; Kurahara, D; Swedo, SE1
Chen, WH; Ho, CW; Ho, MJ; Lin, CH; Liu, TW; Popat, SD; Tsai, KC; Yang, AS1
Gloster, TM; Macauley, MS; Shan, X; Vocadlo, DJ; Yuzwa, SA1
Almanasra, A; Havranek, B; Islam, SM1

Reviews

2 review(s) available for acetylglucosamine and g(m2) ganglioside

ArticleYear
Lysosomal storage diseases in adults.
    Pathology, research and practice, 1994, Volume: 190, Issue:8

    Topics: Acetylglucosamine; Adult; Age of Onset; Aspartylglucosaminuria; G(M2) Ganglioside; Gangliosidoses; Gangliosidosis, GM1; Gaucher Disease; Humans; Leukodystrophy, Metachromatic

1994
Streptococcal mimicry and antibody-mediated cell signaling in the pathogenesis of Sydenham's chorea.
    Autoimmunity, 2006, Volume: 39, Issue:1

    Topics: Acetylglucosamine; Animals; Antibodies; Chorea; G(M2) Ganglioside; Humans; Molecular Mimicry; Signal Transduction; Streptococcal Infections

2006

Other Studies

8 other study(ies) available for acetylglucosamine and g(m2) ganglioside

ArticleYear
Biochemical characterization of beta-hexosaminidase in different biological specimens from eleven patients with GM2-gangliosidosis B1 variant.
    Journal of inherited metabolic disease, 1991, Volume: 14, Issue:5

    Topics: Acetylglucosamine; beta-N-Acetylhexosaminidases; Child; Child, Preschool; Electrophoresis, Cellulose Acetate; Fibroblasts; G(M2) Ganglioside; Gangliosidoses; Genetic Variation; Heterozygote; Homozygote; Humans; Hymecromone; Leukocytes; Lymphocytes; Portugal

1991
Differentiation of two variants of type-AB GM2-gangliosidosis using chromogenic substrates.
    American journal of human genetics, 1983, Volume: 35, Issue:3

    Topics: Acetylglucosamine; beta-N-Acetylhexosaminidases; Brain; Child, Preschool; Chromogenic Compounds; G(M2) Ganglioside; Hexosaminidases; Humans; Tay-Sachs Disease

1983
Diagnosis of infantile and juvenile forms of GM2 gangliosidosis variant 0. Residual activities toward natural and different synthetic substrates.
    Human genetics, 1984, Volume: 67, Issue:4

    Topics: Acetylglucosamine; Cells, Cultured; Fibroblasts; G(M2) Ganglioside; Gangliosidoses; Genetic Variation; Glucosamine; Hexosaminidases; Humans; Hymecromone; Isoelectric Focusing; Skin; Substrate Specificity

1984
Interaction of activating protein and surfactants with human liver hexosaminidase A and GM2 ganglioside.
    The Biochemical journal, 1980, Mar-01, Volume: 185, Issue:3

    Topics: Acetylglucosamine; Enzyme Activation; G(M2) Ganglioside; Gangliosides; Glucosides; Glycoproteins; Hexosaminidases; Humans; Hydrolysis; Hymecromone; Kinetics; Liver; Proteins; Saposins; Sphingolipid Activator Proteins; Surface-Active Agents

1980
Specific induction of macrophage inflammatory protein 1-alpha in glial cells of Sandhoff disease model mice associated with accumulation of N-acetylhexosaminyl glycoconjugates.
    Journal of neurochemistry, 2005, Volume: 92, Issue:6

    Topics: Acetylglucosamine; Animals; Astrocytes; beta-N-Acetylhexosaminidases; Brain; Calcium-Binding Proteins; Chemokine CCL3; Chemokine CCL4; Chemokines; Disease Models, Animal; Disease Progression; G(M2) Ganglioside; Gene Expression Regulation; Glial Fibrillary Acidic Protein; Glycoconjugates; Hexosaminidase A; Hexosaminidase B; Macrophage Inflammatory Proteins; Mice; Mice, Inbred C57BL; Mice, Knockout; Microfilament Proteins; Microglia; Neuroglia; Protein Subunits; RNA, Messenger; Sandhoff Disease; Up-Regulation

2005
Development of GlcNAc-inspired iminocyclitiols as potent and selective N-acetyl-beta-hexosaminidase inhibitors.
    ACS chemical biology, 2010, May-21, Volume: 5, Issue:5

    Topics: Acetylglucosamine; Animals; beta-N-Acetylhexosaminidases; Blotting, Western; Cell Line; Enzyme Inhibitors; Fluorescent Antibody Technique; G(M2) Ganglioside; Glycosphingolipids; Humans; Immunohistochemistry; Kinetics; Mice; Microglia; Models, Molecular; Oximes; Phenylcarbamates; Streptozocin

2010
Elevation of Global O-GlcNAc in rodents using a selective O-GlcNAcase inhibitor does not cause insulin resistance or perturb glucohomeostasis.
    Chemistry & biology, 2010, Sep-24, Volume: 17, Issue:9

    Topics: Acetylglucosamine; Animals; beta-N-Acetylhexosaminidases; Bridged Bicyclo Compounds, Heterocyclic; Enzyme Inhibitors; G(M2) Ganglioside; Glucose; Insulin Resistance; Mice; Rats; Rats, Sprague-Dawley; Signal Transduction

2010
In-silico screening and microsecond molecular dynamics simulations to identify single point mutations that destabilize β-hexosaminidase A causing Tay-Sachs disease.
    Proteins, 2021, Volume: 89, Issue:11

    Topics: Acetylglucosamine; beta-Hexosaminidase alpha Chain; Binding Sites; Central Nervous System; G(M2) Ganglioside; Gene Expression; Humans; Hydrogen Bonding; Molecular Dynamics Simulation; Neurons; Peripheral Nervous System; Point Mutation; Polymorphism, Single Nucleotide; Protein Binding; Protein Conformation, alpha-Helical; Protein Conformation, beta-Strand; Protein Interaction Domains and Motifs; Tay-Sachs Disease; Thermodynamics; Thiazoles

2021