acetylcysteine and ethylmalonic acid

acetylcysteine has been researched along with ethylmalonic acid in 3 studies

Research

Studies (3)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's3 (100.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Burlina, AB; Dweikat, I; Hildebrandt, T; Lamperti, C; Savoiardo, M; Tiranti, V; Viscomi, C; Zeviani, M1
Amaral, AU; Hickmann, FH; Kleemann, D; Ribeiro, CA; Ritter, L; Sitta, Â; Wajner, M1
Abdenur, JE; Boyer, M; Di Meo, I; Eftekharian, S; Sowa, M; Steenari, MR; Tiranti, V1

Other Studies

3 other study(ies) available for acetylcysteine and ethylmalonic acid

ArticleYear
Combined treatment with oral metronidazole and N-acetylcysteine is effective in ethylmalonic encephalopathy.
    Nature medicine, 2010, Volume: 16, Issue:8

    Topics: Acetylcysteine; Administration, Oral; Animals; Anti-Infective Agents; Brain Diseases, Metabolic, Inborn; Child, Preschool; Dioxygenases; Drug Combinations; Drug Evaluation, Preclinical; Female; Humans; Infant; Male; Malonates; Metronidazole; Mice; Mice, Knockout; Mitochondrial Proteins; Treatment Outcome

2010
Disturbance of energy and redox homeostasis and reduction of Na+,K+-ATPase activity provoked by in vivo intracerebral administration of ethylmalonic acid to young rats.
    Biochimica et biophysica acta, 2015, Volume: 1852, Issue:5

    Topics: Acetylcysteine; Animals; Antioxidants; Carbon Dioxide; Corpus Striatum; Electron Transport Complex II; Electron Transport Complex III; Energy Metabolism; Glucose; Glutathione; Homeostasis; Injections, Intraventricular; Lactates; Male; Malonates; Malondialdehyde; Melatonin; Oxidation-Reduction; Rats, Wistar; Sodium-Potassium-Exchanging ATPase; Synapses

2015
Response to medical and a novel dietary treatment in newborn screen identified patients with ethylmalonic encephalopathy.
    Molecular genetics and metabolism, 2018, Volume: 124, Issue:1

    Topics: Acetylcysteine; Amino Acids; Biomarkers; Brain Diseases, Metabolic, Inborn; Cysteine; Diet; Female; Humans; Infant; Infant, Newborn; Lactic Acid; Male; Malonates; Methionine; Metronidazole; Mitochondrial Proteins; Mutation; Neonatal Screening; Nucleocytoplasmic Transport Proteins; Purpura; Sulfur

2018