Page last updated: 2024-08-21

3-methylglutaric acid and valerates

3-methylglutaric acid has been researched along with valerates in 8 studies

Research

Studies (8)

TimeframeStudies, this research(%)All Research%
pre-19902 (25.00)18.7374
1990's0 (0.00)18.2507
2000's4 (50.00)29.6817
2010's2 (25.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Beemer, FA; Bruinvis, L; Duran, M; Ketting, D; Tibosch, AS; Wadman, SK1
Berry, HK; Denton, MD; Norman, EJ1
Brandis, M; Ensenauer, R; Gibson, KM; Lehnert, W; Müller, CB; Schwab, KO1
Engelke, UF; Kluijtmans, LA; Kremer, B; Loss, S; Loupatty, FJ; Morava, E; Moskau, D; van den Bergh, E; van der Graaf, M; Wanders, RJ; Wevers, RA1
Amaral, AU; de Bortoli, G; Latini, A; Leipnitz, G; Schuck, PF; Seminotti, B; Solano, A; Wajner, M; Wannmacher, CM; Wyse, AT1
Amaral, AU; Beskow, AP; da Silva, Lde B; Fernandes, CG; Leipnitz, G; Ribeiro, CA; Seminotti, B; Vargas, CR; Wajner, M; Zanatta, A1
Hickmann, FH; Ribeiro, CA; Wajner, M1
Acquaviva-Bourdain, C; Briand, G; Dobbelaere, D; Fontaine, M; Jissendi-Tchofo, P; Mention, K; Roland, D; Ultré, V; Vamecq, J1

Other Studies

8 other study(ies) available for 3-methylglutaric acid and valerates

ArticleYear
Inherited 3-methylglutaconic aciduria in two brothers--another defect of leucine metabolism.
    The Journal of pediatrics, 1982, Volume: 101, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Glutarates; Humans; Hydro-Lyases; Leucine; Male; Meglutol; Speech Disorders; Valerates

1982
Gas-chromatographic/mass spectrometric detection of 3-hydroxy-3-methylglutaryl-CoA lyase deficiency in double first cousins.
    Clinical chemistry, 1982, Volume: 28, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Female; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Hydroxy Acids; Infant; Leucine; Male; Meglutol; Oxo-Acid-Lyases; Valerates

1982
3-Methylglutaconyl-CoA hydratase deficiency: a new patient with speech retardation as the leading sign.
    Journal of inherited metabolic disease, 2000, Volume: 23, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Diet, Protein-Restricted; Fibroblasts; Glutarates; Humans; Hydro-Lyases; Meglutol; Speech Disorders; Valerates

2000
NMR spectroscopic studies on the late onset form of 3-methylglutaconic aciduria type I and other defects in leucine metabolism.
    NMR in biomedicine, 2006, Volume: 19, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Brain; Female; Glutarates; Humans; Leucine; Magnetic Resonance Spectroscopy; Meglutol; Middle Aged; Valerates

2006
Induction of oxidative stress by the metabolites accumulating in 3-methylglutaconic aciduria in cerebral cortex of young rats.
    Life sciences, 2008, Mar-12, Volume: 82, Issue:11-12

    Topics: Animals; Antioxidants; Cerebral Cortex; Glutarates; Glutathione; Lipid Peroxidation; Meglutol; Mitochondria; Molecular Structure; Oxidants; Oxidative Stress; Protein Carbonylation; Rats; Rats, Wistar; Superoxides; Thiobarbituric Acid Reactive Substances; Valerates

2008
Striatum is more vulnerable to oxidative damage induced by the metabolites accumulating in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency as compared to liver.
    International journal of developmental neuroscience : the official journal of the International Society for Developmental Neuroscience, 2009, Volume: 27, Issue:4

    Topics: Animals; Corpus Striatum; Glutarates; Glutathione; Glycine; Humans; Liver; Male; Meglutol; Oxidative Stress; Oxo-Acid-Lyases; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances; Valerates

2009
Neurochemical evidence that 3-methylglutaric acid inhibits synaptic Na+,K+-ATPase activity probably through oxidative damage in brain cortex of young rats.
    International journal of developmental neuroscience : the official journal of the International Society for Developmental Neuroscience, 2011, Volume: 29, Issue:1

    Topics: Animals; Cerebral Cortex; Glutarates; Humans; Male; Meglutol; Mitochondria; Oxidation-Reduction; Oxidative Stress; Rats; Rats, Wistar; Sodium-Potassium-Exchanging ATPase; Synaptic Membranes; Valerates

2011
Coupled brain and urine spectroscopy - in vivo metabolomic characterization of HMG-CoA lyase deficiency in 5 patients.
    Molecular genetics and metabolism, 2017, Volume: 121, Issue:2

    Topics: Acetyl-CoA C-Acetyltransferase; Amino Acid Metabolism, Inborn Errors; Brain; Brain Chemistry; Cerebellum; Child; Child, Preschool; Female; Humans; Hydrogen-Ion Concentration; Infant; Infant, Newborn; Magnetic Resonance Imaging; Male; Meglutol; Metabolomics; Proton Magnetic Resonance Spectroscopy; Urine; Valerates; White Matter

2017