3-hydroxyisobutyric acid has been researched along with valine in 6 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 2 (33.33) | 18.7374 |
1990's | 2 (33.33) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 2 (33.33) | 2.80 |
Authors | Studies |
---|---|
Barshop, B; Ko, FJ; Nyhan, WL; Sweetman, L; Wolff, J | 1 |
Brosnan, JT; Brosnan, ME; Letto, J | 1 |
Congdon, PJ; Green, A; Haigh, D; Pollitt, RJ; Smith, R | 1 |
Yoshida, I | 1 |
Biskup, S; Fobker, M; Hollenbeck, JC; Linden, M; Marquardt, T; Meyer, M; Och, U; Reunert, J; Rust, S; Sass, JO; Seelhöfer, A | 1 |
Al-Hertani, W; Donati, MA; Ferdinandusse, S; Fung, E; Koster, J; Marquardt, T; Pasquini, E; Reeves, M; Rombough, C; Ruiter, JPN; Sasarman, F; Sass, JO; Sinasac, DS; Sparkes, R; Voit, R; Wanders, RJA; Waterham, HR | 1 |
1 review(s) available for 3-hydroxyisobutyric acid and valine
Article | Year |
---|---|
[3-Hydroxyisobutyric aciduria (3-hydroxyisobutyric acid dehydrogenase deficiency)].
Topics: Amino Acid Metabolism, Inborn Errors; Diagnosis, Differential; Humans; Hydroxybutyrates; Prognosis; Valine | 1998 |
5 other study(ies) available for 3-hydroxyisobutyric acid and valine
Article | Year |
---|---|
3-Hydroxyisobutyric aciduria: an inborn error of valine metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Child; Humans; Hydroxybutyrates; Male; Valine | 1991 |
Valine metabolism. Gluconeogenesis from 3-hydroxyisobutyrate.
Topics: Animals; Gluconeogenesis; Hydroxybutyrates; In Vitro Techniques; Kidney Cortex; Kidney Tubules; Liver; Male; Rats; Rats, Inbred Strains; Valine | 1986 |
Hypermethioninaemia and 3-hydroxyisobutyric aciduria in an apparently healthy baby.
Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Aminoisobutyric Acids; Humans; Hydroxybutyrates; Infant; Isomerism; Lactates; Lactic Acid; Methionine; Thymine; Valine | 1981 |
3-Hydroxyisobutyrate dehydrogenase (HIBADH) deficiency-A novel disorder of valine metabolism.
Topics: Alcohol Oxidoreductases; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Diagnosis, Differential; Female; Humans; Hydroxybutyrates; Infant; Male; Valine | 2021 |
3-Hydroxyisobutyric acid dehydrogenase deficiency: Expanding the clinical spectrum and quantitation of D- and L-3-Hydroxyisobutyric acid by an LC-MS/MS method.
Topics: Amino Acid Metabolism, Inborn Errors; Chromatography, Liquid; Humans; Hydroxybutyrates; Oxidoreductases; Tandem Mass Spectrometry; Valine | 2022 |