3-hydroxyisobutyric acid and valine

3-hydroxyisobutyric acid has been researched along with valine in 6 studies

Research

Studies (6)

TimeframeStudies, this research(%)All Research%
pre-19902 (33.33)18.7374
1990's2 (33.33)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's2 (33.33)2.80

Authors

AuthorsStudies
Barshop, B; Ko, FJ; Nyhan, WL; Sweetman, L; Wolff, J1
Brosnan, JT; Brosnan, ME; Letto, J1
Congdon, PJ; Green, A; Haigh, D; Pollitt, RJ; Smith, R1
Yoshida, I1
Biskup, S; Fobker, M; Hollenbeck, JC; Linden, M; Marquardt, T; Meyer, M; Och, U; Reunert, J; Rust, S; Sass, JO; Seelhöfer, A1
Al-Hertani, W; Donati, MA; Ferdinandusse, S; Fung, E; Koster, J; Marquardt, T; Pasquini, E; Reeves, M; Rombough, C; Ruiter, JPN; Sasarman, F; Sass, JO; Sinasac, DS; Sparkes, R; Voit, R; Wanders, RJA; Waterham, HR1

Reviews

1 review(s) available for 3-hydroxyisobutyric acid and valine

ArticleYear
[3-Hydroxyisobutyric aciduria (3-hydroxyisobutyric acid dehydrogenase deficiency)].
    Ryoikibetsu shokogun shirizu, 1998, Issue:18 Pt 1

    Topics: Amino Acid Metabolism, Inborn Errors; Diagnosis, Differential; Humans; Hydroxybutyrates; Prognosis; Valine

1998

Other Studies

5 other study(ies) available for 3-hydroxyisobutyric acid and valine

ArticleYear
3-Hydroxyisobutyric aciduria: an inborn error of valine metabolism.
    Pediatric research, 1991, Volume: 30, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Child; Humans; Hydroxybutyrates; Male; Valine

1991
Valine metabolism. Gluconeogenesis from 3-hydroxyisobutyrate.
    The Biochemical journal, 1986, Dec-15, Volume: 240, Issue:3

    Topics: Animals; Gluconeogenesis; Hydroxybutyrates; In Vitro Techniques; Kidney Cortex; Kidney Tubules; Liver; Male; Rats; Rats, Inbred Strains; Valine

1986
Hypermethioninaemia and 3-hydroxyisobutyric aciduria in an apparently healthy baby.
    Journal of inherited metabolic disease, 1981, Volume: 4, Issue:2

    Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Aminoisobutyric Acids; Humans; Hydroxybutyrates; Infant; Isomerism; Lactates; Lactic Acid; Methionine; Thymine; Valine

1981
3-Hydroxyisobutyrate dehydrogenase (HIBADH) deficiency-A novel disorder of valine metabolism.
    Journal of inherited metabolic disease, 2021, Volume: 44, Issue:6

    Topics: Alcohol Oxidoreductases; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Diagnosis, Differential; Female; Humans; Hydroxybutyrates; Infant; Male; Valine

2021
3-Hydroxyisobutyric acid dehydrogenase deficiency: Expanding the clinical spectrum and quantitation of D- and L-3-Hydroxyisobutyric acid by an LC-MS/MS method.
    Journal of inherited metabolic disease, 2022, Volume: 45, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Chromatography, Liquid; Humans; Hydroxybutyrates; Oxidoreductases; Tandem Mass Spectrometry; Valine

2022