Page last updated: 2024-09-04

2-methylacetoacetic acid and alpha-methyl-beta-hydroxybutyrate

2-methylacetoacetic acid has been researched along with alpha-methyl-beta-hydroxybutyrate in 6 studies

Compound Research Comparison

Studies
(2-methylacetoacetic acid)
Trials
(2-methylacetoacetic acid)
Recent Studies (post-2010)
(2-methylacetoacetic acid)
Studies
(alpha-methyl-beta-hydroxybutyrate)
Trials
(alpha-methyl-beta-hydroxybutyrate)
Recent Studies (post-2010) (alpha-methyl-beta-hydroxybutyrate)
9022305

Research

Studies (6)

TimeframeStudies, this research(%)All Research%
pre-19902 (33.33)18.7374
1990's0 (0.00)18.2507
2000's2 (33.33)29.6817
2010's2 (33.33)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Leonard, JV; Middleton, B; Seakins, JW1
Bartlett, K; Middleton, B1
Fukao, T; Hazama, A; Kohno, Y; Kondo, M; Kondo, N; Kubo, T; Matsuo, N; Sakura, N; Shigematsu, Y; Yamaga, H; Yamaguchi, S; Zhang, GX1
da C Ferreira, G; Dalcin, KB; de Assis, DR; Filho, CS; Latini, A; Leipnitz, G; Maria, RC; Perry, ML; Ribeiro, CA; Rosa, RB; Schuck, PF; Wajner, M; Wannmacher, CM; Wyse, AT1
Amaral, AU; Dutra-Filho, CS; Fernandes, CG; Leipnitz, G; Seminotti, B; Wajner, M1
Bancel, LP; Dessein, AF; Germain, N; Guemann, AS; Joncquel Chevalier Curt, M1

Other Studies

6 other study(ies) available for 2-methylacetoacetic acid and alpha-methyl-beta-hydroxybutyrate

ArticleYear
Acetoacetyl CoA thiolase deficiency presenting as ketotic hypoglycemia.
    Pediatric research, 1987, Volume: 21, Issue:2

    Topics: Acetoacetates; Acetyl-CoA C-Acetyltransferase; Acetyltransferases; Acidosis; Female; Glycine; Humans; Hydroxybutyrates; Hypoglycemia; Infant; Ketosis

1987
The synthesis and characterisation of 2-methylacetoacetyl coenzyme A and its use in the identification of the site of the defect in 2-methylacetoacetic and 2-methyl-3-hydroxybutyric aciduria.
    Clinica chimica acta; international journal of clinical chemistry, 1983, Mar-14, Volume: 128, Issue:2-3

    Topics: Acetoacetates; Acetyl-CoA C-Acetyltransferase; Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Child, Preschool; Fibroblasts; Humans; Hydroxybutyrates; Isoleucine

1983
The mitochondrial acetoacetyl-CoA thiolase (T2) deficiency in Japanese patients: urinary organic acid and blood acylcarnitine profiles under stable conditions have subtle abnormalities in T2-deficient patients with some residual T2 activity.
    Journal of inherited metabolic disease, 2003, Volume: 26, Issue:5

    Topics: Acetoacetates; Acetyl-CoA C-Acetyltransferase; Amino Acid Metabolism, Inborn Errors; Carnitine; Humans; Hydroxybutyrates; Infant; Isoleucine; Ketone Bodies; Male; Mitochondria; Mutation

2003
Inhibition of energy metabolism by 2-methylacetoacetate and 2-methyl-3-hydroxybutyrate in cerebral cortex of developing rats.
    Journal of inherited metabolic disease, 2005, Volume: 28, Issue:4

    Topics: 3-Hydroxyacyl CoA Dehydrogenases; Acetates; Acetoacetates; Acetyl-CoA C-Acyltransferase; Acidosis; Alcohol Oxidoreductases; Animals; Brain; Carbon Dioxide; Cerebral Cortex; Citrates; Creatine Kinase; Dose-Response Relationship, Drug; Electron Transport; Energy Metabolism; Glucose; Glutathione; Glycine; Hydroxybutyrates; In Vitro Techniques; Intellectual Disability; Lactic Acid; NG-Nitroarginine Methyl Ester; Oxygen; Rats; Rats, Wistar; Time Factors

2005
Evidence that 2-methylacetoacetate induces oxidative stress in rat brain.
    Metabolic brain disease, 2010, Volume: 25, Issue:3

    Topics: Acetoacetates; Animals; Brain; Brain Diseases, Metabolic; Cerebral Cortex; Hydroxybutyrates; Lipid Peroxidation; Oxidative Stress; Rats; Rats, Wistar

2010
Abnormal Ketone Bodies in a 22-Month-Old Boy Presenting with Recurrent Vomiting and Metabolic Acidosis.
    Clinical chemistry, 2019, Volume: 65, Issue:11

    Topics: Acetoacetates; Acetyl-CoA C-Acyltransferase; Acidosis; Amino Acid Metabolism, Inborn Errors; Glycine; Humans; Hydroxybutyrates; Infant; Ketone Bodies; Male; Vomiting

2019