2-ethylhydracrylic acid has been researched along with valerates in 11 studies
Studies (2-ethylhydracrylic acid) | Trials (2-ethylhydracrylic acid) | Recent Studies (post-2010) (2-ethylhydracrylic acid) | Studies (valerates) | Trials (valerates) | Recent Studies (post-2010) (valerates) |
---|---|---|---|---|---|
12 | 0 | 3 | 2,251 | 294 | 457 |
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 4 (36.36) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 4 (36.36) | 29.6817 |
2010's | 3 (27.27) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Klassen, GA; Mamer, OA; Scriver, CR; Tjoa, SS | 1 |
Green, A; Pollitt, RJ; Smith, R | 1 |
Mamer, OA; Tjoa, SS | 1 |
Jakobs, C; Nyhan, WL; Sweetman, L | 1 |
Bergh, JJ; Castagnoli, N; Mienie, LJ; Petzer, JP; Van der Schyf, CJ | 1 |
Andresen, BS; Boneh, A; Gutman, A; Korman, SH; Pitt, JJ; Zeharia, A | 1 |
Andresen, BS; Engel, K; Ensenauer, R; Häberle, J; Lehnert, W; Mégarbané, A; Reich, H; Röschinger, W; Sass, JO; Schirrmacher, O; Steuerwald, U; Zschocke, J | 1 |
Baldellou, A; Briones, P; Campistol, J; Cortés, N; Delpiccolo, C; Fernández, C; Fons, C; Fuentes-Castelló, MA; García-Villoria, J; González, I; Hernández-Gonzalez, A; Messeguer, A; Navarro-Sastre, A; Pérez-Cerdá, C; Ribes, A | 1 |
Ryan, RO | 1 |
Böhmer, D; Chandoga, J; Konkoľová, J; Kováčik, J; Kramarová, V; Paučinová, I; Repiský, M | 1 |
Antonetti, G; Boenzi, S; Carrozzo, R; Catesini, G; Diodato, D; Dionisi-Vici, C; Martinelli, D; Olivieri, G; Rizzo, C; Sacchetti, E; Semeraro, M | 1 |
1 review(s) available for 2-ethylhydracrylic acid and valerates
Article | Year |
---|---|
Metabolic annotation of 2-ethylhydracrylic acid.
Topics: Animals; Barth Syndrome; Humans; Multiple Acyl Coenzyme A Dehydrogenase Deficiency; Valerates | 2015 |
10 other study(ies) available for 2-ethylhydracrylic acid and valerates
Article | Year |
---|---|
Demonstration of a new mammalian isoleucine catabolic pathway yielding an Rseries of metabolites.
Topics: Acrylates; Animals; Butyrates; Dogs; Female; Humans; Hydroxy Acids; Isoleucine; Male; Malonates; Rabbits; Rats; Time Factors; Valerates | 1976 |
Excessive excretion of beta-alanine and of 3-hydroxypropionic, R- and S-3-aminoisobutyric, R- and S-3-hydroxyisobutyric and S-2-(hydroxymethyl)butyric acids probably due to a defect in the metabolism of the corresponding malonic semialdehydes.
Topics: Alanine; Aldehyde Oxidoreductases; Amino Acid Metabolism, Inborn Errors; Aminoisobutyric Acids; beta-Alanine; Child, Preschool; Humans; Hydroxybutyrates; Lactates; Lactic Acid; Male; Malonate-Semialdehyde Dehydrogenase (Acetylating); Malonates; Malondialdehyde; Methylmalonate-Semialdehyde Dehydrogenase (Acylating); Valerates | 1985 |
2-Ethylhydracrylic acid: a newly described urinary organic acid.
Topics: Acyltransferases; Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Coenzyme A; Humans; Hydroxy Acids; Hydroxybutyrates; Isoleucine; Keto Acids; Malonates; Mass Spectrometry; Valerates | 1974 |
Hydroxy acid metabolites of branched-chain amino acids in amniotic fluid.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Amniotic Fluid; Caproates; Female; Gas Chromatography-Mass Spectrometry; Humans; Hydroxy Acids; Hydroxybutyrates; Maple Syrup Urine Disease; Methylmalonic Acid; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Valerates | 1984 |
Metabolic defects caused by 1-methyl-4-phenyl-1,2,3,6-tetrahydropyridine (MPTP) and by HPTP (the tetrahydropyridinyl analog of haloperidol), in rats.
Topics: 1-Methyl-4-phenyl-1,2,3,6-tetrahydropyridine; Animals; Antipsychotic Agents; Haloperidol; Lactic Acid; Male; Metabolism, Inborn Errors; Mitochondria; Oxygen Consumption; Rats; Rats, Sprague-Dawley; Valerates | 2000 |
2-ethylhydracrylic aciduria in short/branched-chain acyl-CoA dehydrogenase deficiency: application to diagnosis and implications for the R-pathway of isoleucine oxidation.
Topics: Biomarkers; Butyrates; Butyryl-CoA Dehydrogenase; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant, Newborn; Isoleucine; Mutation; Oxidation-Reduction; Stereoisomerism; Valerates | 2005 |
2-Methylbutyryl-coenzyme A dehydrogenase deficiency: functional and molecular studies on a defect in isoleucine catabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Butyryl-CoA Dehydrogenase; Cells, Cultured; Child; Child, Preschool; Female; Genotype; Glycine; Humans; Infant; Isoleucine; Male; Metabolism; Valerates | 2008 |
Study of patients and carriers with 2-methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD) deficiency: difficulties in the diagnosis.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Alcohol Oxidoreductases; Amino Acid Metabolism, Inborn Errors; Female; Glycine; Heredodegenerative Disorders, Nervous System; Humans; Hydroxybutyrates; Infant; Infant, Newborn; Male; Valerates | 2009 |
Severe child form of primary hyperoxaluria type 2 - a case report revealing consequence of GRHPR deficiency on metabolism.
Topics: Alcohol Oxidoreductases; Aminoisobutyric Acids; DNA Mutational Analysis; Female; Gas Chromatography-Mass Spectrometry; Humans; Hydroxybutyrates; Hyperoxaluria, Primary; Infant; Lactic Acid; Urolithiasis; Valerates | 2017 |
The urinary organic acids profile in single large-scale mitochondrial DNA deletion disorders.
Topics: 3-Hydroxybutyric Acid; Acyl-CoA Dehydrogenase, Long-Chain; Adolescent; Child; Child, Preschool; Congenital Bone Marrow Failure Syndromes; DNA, Mitochondrial; Fumarates; Glutarates; Humans; Hydroxybutyrates; Infant; Kearns-Sayre Syndrome; Lactic Acid; Lipid Metabolism, Inborn Errors; Mitochondrial Diseases; Muscular Diseases; Pyruvic Acid; Retrospective Studies; Valerates | 2018 |