Page last updated: 2024-09-05

2-ethylhydracrylic acid and valerates

2-ethylhydracrylic acid has been researched along with valerates in 11 studies

Compound Research Comparison

Studies
(2-ethylhydracrylic acid)
Trials
(2-ethylhydracrylic acid)
Recent Studies (post-2010)
(2-ethylhydracrylic acid)
Studies
(valerates)
Trials
(valerates)
Recent Studies (post-2010) (valerates)
12032,251294457

Research

Studies (11)

TimeframeStudies, this research(%)All Research%
pre-19904 (36.36)18.7374
1990's0 (0.00)18.2507
2000's4 (36.36)29.6817
2010's3 (27.27)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Klassen, GA; Mamer, OA; Scriver, CR; Tjoa, SS1
Green, A; Pollitt, RJ; Smith, R1
Mamer, OA; Tjoa, SS1
Jakobs, C; Nyhan, WL; Sweetman, L1
Bergh, JJ; Castagnoli, N; Mienie, LJ; Petzer, JP; Van der Schyf, CJ1
Andresen, BS; Boneh, A; Gutman, A; Korman, SH; Pitt, JJ; Zeharia, A1
Andresen, BS; Engel, K; Ensenauer, R; Häberle, J; Lehnert, W; Mégarbané, A; Reich, H; Röschinger, W; Sass, JO; Schirrmacher, O; Steuerwald, U; Zschocke, J1
Baldellou, A; Briones, P; Campistol, J; Cortés, N; Delpiccolo, C; Fernández, C; Fons, C; Fuentes-Castelló, MA; García-Villoria, J; González, I; Hernández-Gonzalez, A; Messeguer, A; Navarro-Sastre, A; Pérez-Cerdá, C; Ribes, A1
Ryan, RO1
Böhmer, D; Chandoga, J; Konkoľová, J; Kováčik, J; Kramarová, V; Paučinová, I; Repiský, M1
Antonetti, G; Boenzi, S; Carrozzo, R; Catesini, G; Diodato, D; Dionisi-Vici, C; Martinelli, D; Olivieri, G; Rizzo, C; Sacchetti, E; Semeraro, M1

Reviews

1 review(s) available for 2-ethylhydracrylic acid and valerates

ArticleYear
Metabolic annotation of 2-ethylhydracrylic acid.
    Clinica chimica acta; international journal of clinical chemistry, 2015, Aug-25, Volume: 448

    Topics: Animals; Barth Syndrome; Humans; Multiple Acyl Coenzyme A Dehydrogenase Deficiency; Valerates

2015

Other Studies

10 other study(ies) available for 2-ethylhydracrylic acid and valerates

ArticleYear
Demonstration of a new mammalian isoleucine catabolic pathway yielding an Rseries of metabolites.
    The Biochemical journal, 1976, Dec-15, Volume: 160, Issue:3

    Topics: Acrylates; Animals; Butyrates; Dogs; Female; Humans; Hydroxy Acids; Isoleucine; Male; Malonates; Rabbits; Rats; Time Factors; Valerates

1976
Excessive excretion of beta-alanine and of 3-hydroxypropionic, R- and S-3-aminoisobutyric, R- and S-3-hydroxyisobutyric and S-2-(hydroxymethyl)butyric acids probably due to a defect in the metabolism of the corresponding malonic semialdehydes.
    Journal of inherited metabolic disease, 1985, Volume: 8, Issue:2

    Topics: Alanine; Aldehyde Oxidoreductases; Amino Acid Metabolism, Inborn Errors; Aminoisobutyric Acids; beta-Alanine; Child, Preschool; Humans; Hydroxybutyrates; Lactates; Lactic Acid; Male; Malonate-Semialdehyde Dehydrogenase (Acetylating); Malonates; Malondialdehyde; Methylmalonate-Semialdehyde Dehydrogenase (Acylating); Valerates

1985
2-Ethylhydracrylic acid: a newly described urinary organic acid.
    Clinica chimica acta; international journal of clinical chemistry, 1974, Sep-16, Volume: 55, Issue:2

    Topics: Acyltransferases; Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Coenzyme A; Humans; Hydroxy Acids; Hydroxybutyrates; Isoleucine; Keto Acids; Malonates; Mass Spectrometry; Valerates

1974
Hydroxy acid metabolites of branched-chain amino acids in amniotic fluid.
    Clinica chimica acta; international journal of clinical chemistry, 1984, Jul-16, Volume: 140, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Amniotic Fluid; Caproates; Female; Gas Chromatography-Mass Spectrometry; Humans; Hydroxy Acids; Hydroxybutyrates; Maple Syrup Urine Disease; Methylmalonic Acid; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Valerates

1984
Metabolic defects caused by 1-methyl-4-phenyl-1,2,3,6-tetrahydropyridine (MPTP) and by HPTP (the tetrahydropyridinyl analog of haloperidol), in rats.
    Life sciences, 2000, Apr-07, Volume: 66, Issue:20

    Topics: 1-Methyl-4-phenyl-1,2,3,6-tetrahydropyridine; Animals; Antipsychotic Agents; Haloperidol; Lactic Acid; Male; Metabolism, Inborn Errors; Mitochondria; Oxygen Consumption; Rats; Rats, Sprague-Dawley; Valerates

2000
2-ethylhydracrylic aciduria in short/branched-chain acyl-CoA dehydrogenase deficiency: application to diagnosis and implications for the R-pathway of isoleucine oxidation.
    Clinical chemistry, 2005, Volume: 51, Issue:3

    Topics: Biomarkers; Butyrates; Butyryl-CoA Dehydrogenase; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant, Newborn; Isoleucine; Mutation; Oxidation-Reduction; Stereoisomerism; Valerates

2005
2-Methylbutyryl-coenzyme A dehydrogenase deficiency: functional and molecular studies on a defect in isoleucine catabolism.
    Molecular genetics and metabolism, 2008, Volume: 93, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Butyryl-CoA Dehydrogenase; Cells, Cultured; Child; Child, Preschool; Female; Genotype; Glycine; Humans; Infant; Isoleucine; Male; Metabolism; Valerates

2008
Study of patients and carriers with 2-methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD) deficiency: difficulties in the diagnosis.
    Clinical biochemistry, 2009, Volume: 42, Issue:1-2

    Topics: 3-Hydroxyacyl CoA Dehydrogenases; Alcohol Oxidoreductases; Amino Acid Metabolism, Inborn Errors; Female; Glycine; Heredodegenerative Disorders, Nervous System; Humans; Hydroxybutyrates; Infant; Infant, Newborn; Male; Valerates

2009
Severe child form of primary hyperoxaluria type 2 - a case report revealing consequence of GRHPR deficiency on metabolism.
    BMC medical genetics, 2017, 05-31, Volume: 18, Issue:1

    Topics: Alcohol Oxidoreductases; Aminoisobutyric Acids; DNA Mutational Analysis; Female; Gas Chromatography-Mass Spectrometry; Humans; Hydroxybutyrates; Hyperoxaluria, Primary; Infant; Lactic Acid; Urolithiasis; Valerates

2017
The urinary organic acids profile in single large-scale mitochondrial DNA deletion disorders.
    Clinica chimica acta; international journal of clinical chemistry, 2018, Volume: 481

    Topics: 3-Hydroxybutyric Acid; Acyl-CoA Dehydrogenase, Long-Chain; Adolescent; Child; Child, Preschool; Congenital Bone Marrow Failure Syndromes; DNA, Mitochondrial; Fumarates; Glutarates; Humans; Hydroxybutyrates; Infant; Kearns-Sayre Syndrome; Lactic Acid; Lipid Metabolism, Inborn Errors; Mitochondrial Diseases; Muscular Diseases; Pyruvic Acid; Retrospective Studies; Valerates

2018