2-aminoadipic acid and pyridoxal phosphate

2-aminoadipic acid has been researched along with pyridoxal phosphate in 6 studies

Research

Studies (6)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's3 (50.00)29.6817
2010's2 (33.33)24.3611
2020's1 (16.67)2.80

Authors

AuthorsStudies
Erwa, W; Jakobs, C; Paschke, E; Plecko, B; Stöckler-Ipsiroglu, S; Struys, EA1
Fushinobu, S; Kuzuyama, T; Miyagawa, T; Miyazaki, T; Nishiyama, M; Tomita, T1
Kuzuyama, T; Miyagawa, T; Nishiyama, M; Ouchi, T; Tomita, T1
Al Shahwan, S; Bakkali, A; Nota, B; Salomons, GS; Struys, EA; Tabarki, B1
Arruda, P; Eberlin, MN; Laranjeira, ÂB; MacKenzie, A; Marques, LA; Pena, IA; Yunes, JA1
Bouchereau, J; Schiff, M1

Reviews

1 review(s) available for 2-aminoadipic acid and pyridoxal phosphate

ArticleYear
Inherited Disorders of Lysine Metabolism: A Review.
    The Journal of nutrition, 2020, 10-01, Volume: 150, Issue:Suppl 1

    Topics: 2-Aminoadipic Acid; Aldehyde Dehydrogenase; Amino Acid Metabolism, Inborn Errors; Arginine; Brain; Brain Diseases, Metabolic; Brain Diseases, Metabolic, Inborn; Carnitine; Epilepsy; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Lysine; Metabolic Diseases; Pyridoxal Phosphate; Pyridoxine

2020

Other Studies

5 other study(ies) available for 2-aminoadipic acid and pyridoxal phosphate

ArticleYear
Pipecolic acid elevation in plasma and cerebrospinal fluid of two patients with pyridoxine-dependent epilepsy.
    Annals of neurology, 2000, Volume: 48, Issue:1

    Topics: 2-Aminoadipic Acid; Child; Epilepsy; Humans; Infant, Newborn; Male; Picolinic Acids; Pipecolic Acids; Pyridoxal Phosphate; Pyridoxine

2000
Mechanism for multiple-substrates recognition of alpha-aminoadipate aminotransferase from Thermus thermophilus.
    Proteins, 2009, May-01, Volume: 75, Issue:2

    Topics: 2-Aminoadipate Transaminase; 2-Aminoadipic Acid; Enzyme Stability; Hot Temperature; Humans; Leucine; Point Mutation; Protein Conformation; Pyridoxal Phosphate; Structural Homology, Protein; Substrate Specificity; Thermus thermophilus; Transaminases

2009
Dual roles of a conserved pair, Arg23 and Ser20, in recognition of multiple substrates in alpha-aminoadipate aminotransferase from Thermus thermophilus.
    Biochemical and biophysical research communications, 2009, Oct-09, Volume: 388, Issue:1

    Topics: 2-Aminoadipate Transaminase; 2-Aminoadipic Acid; Arginine; Conserved Sequence; Crystallography, X-Ray; Glutamates; Protein Structure, Secondary; Pyridines; Pyridoxal Phosphate; Serine; Substrate Specificity; Thermus thermophilus

2009
Pyridoxine-dependent epilepsy with elevated urinary α-amino adipic semialdehyde in molybdenum cofactor deficiency.
    Pediatrics, 2012, Volume: 130, Issue:6

    Topics: 2-Aminoadipic Acid; Aldehyde Dehydrogenase; Brain; Child, Preschool; Consanguinity; Developmental Disabilities; Diagnosis, Differential; Diffusion Magnetic Resonance Imaging; DNA Mutational Analysis; Electroencephalography; Epilepsy; Exons; Female; Genetic Carrier Screening; Homozygote; Humans; Infant; Infant, Newborn; Leucovorin; Male; Metal Metabolism, Inborn Errors; Molybdoferredoxin; Neurologic Examination; Pyridoxal Phosphate; Pyridoxine; Sequence Analysis, DNA; Sulfurtransferases

2012
Mouse lysine catabolism to aminoadipate occurs primarily through the saccharopine pathway; implications for pyridoxine dependent epilepsy (PDE).
    Biochimica et biophysica acta. Molecular basis of disease, 2017, Volume: 1863, Issue:1

    Topics: 2-Aminoadipic Acid; Animals; Epilepsy; Female; Lysine; Metabolic Networks and Pathways; Mice; Mice, Inbred C57BL; Picolinic Acids; Pyridoxal Phosphate

2017