2-aminoadipic acid has been researched along with pyridoxal phosphate in 6 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 3 (50.00) | 29.6817 |
2010's | 2 (33.33) | 24.3611 |
2020's | 1 (16.67) | 2.80 |
Authors | Studies |
---|---|
Erwa, W; Jakobs, C; Paschke, E; Plecko, B; Stöckler-Ipsiroglu, S; Struys, EA | 1 |
Fushinobu, S; Kuzuyama, T; Miyagawa, T; Miyazaki, T; Nishiyama, M; Tomita, T | 1 |
Kuzuyama, T; Miyagawa, T; Nishiyama, M; Ouchi, T; Tomita, T | 1 |
Al Shahwan, S; Bakkali, A; Nota, B; Salomons, GS; Struys, EA; Tabarki, B | 1 |
Arruda, P; Eberlin, MN; Laranjeira, ÂB; MacKenzie, A; Marques, LA; Pena, IA; Yunes, JA | 1 |
Bouchereau, J; Schiff, M | 1 |
1 review(s) available for 2-aminoadipic acid and pyridoxal phosphate
Article | Year |
---|---|
Inherited Disorders of Lysine Metabolism: A Review.
Topics: 2-Aminoadipic Acid; Aldehyde Dehydrogenase; Amino Acid Metabolism, Inborn Errors; Arginine; Brain; Brain Diseases, Metabolic; Brain Diseases, Metabolic, Inborn; Carnitine; Epilepsy; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Lysine; Metabolic Diseases; Pyridoxal Phosphate; Pyridoxine | 2020 |
5 other study(ies) available for 2-aminoadipic acid and pyridoxal phosphate
Article | Year |
---|---|
Pipecolic acid elevation in plasma and cerebrospinal fluid of two patients with pyridoxine-dependent epilepsy.
Topics: 2-Aminoadipic Acid; Child; Epilepsy; Humans; Infant, Newborn; Male; Picolinic Acids; Pipecolic Acids; Pyridoxal Phosphate; Pyridoxine | 2000 |
Mechanism for multiple-substrates recognition of alpha-aminoadipate aminotransferase from Thermus thermophilus.
Topics: 2-Aminoadipate Transaminase; 2-Aminoadipic Acid; Enzyme Stability; Hot Temperature; Humans; Leucine; Point Mutation; Protein Conformation; Pyridoxal Phosphate; Structural Homology, Protein; Substrate Specificity; Thermus thermophilus; Transaminases | 2009 |
Dual roles of a conserved pair, Arg23 and Ser20, in recognition of multiple substrates in alpha-aminoadipate aminotransferase from Thermus thermophilus.
Topics: 2-Aminoadipate Transaminase; 2-Aminoadipic Acid; Arginine; Conserved Sequence; Crystallography, X-Ray; Glutamates; Protein Structure, Secondary; Pyridines; Pyridoxal Phosphate; Serine; Substrate Specificity; Thermus thermophilus | 2009 |
Pyridoxine-dependent epilepsy with elevated urinary α-amino adipic semialdehyde in molybdenum cofactor deficiency.
Topics: 2-Aminoadipic Acid; Aldehyde Dehydrogenase; Brain; Child, Preschool; Consanguinity; Developmental Disabilities; Diagnosis, Differential; Diffusion Magnetic Resonance Imaging; DNA Mutational Analysis; Electroencephalography; Epilepsy; Exons; Female; Genetic Carrier Screening; Homozygote; Humans; Infant; Infant, Newborn; Leucovorin; Male; Metal Metabolism, Inborn Errors; Molybdoferredoxin; Neurologic Examination; Pyridoxal Phosphate; Pyridoxine; Sequence Analysis, DNA; Sulfurtransferases | 2012 |
Mouse lysine catabolism to aminoadipate occurs primarily through the saccharopine pathway; implications for pyridoxine dependent epilepsy (PDE).
Topics: 2-Aminoadipic Acid; Animals; Epilepsy; Female; Lysine; Metabolic Networks and Pathways; Mice; Mice, Inbred C57BL; Picolinic Acids; Pyridoxal Phosphate | 2017 |