Page last updated: 2024-09-27

Electron Transfer Flavoprotein Alpha Subunit Deficiency

An autosomal recessive disorder of fatty acid oxidation, and branched chain amino acids (AMINO ACIDS, BRANCHED-CHAIN); LYSINE; and CHOLINE catabolism, that is due to defects in either subunit of ELECTRON TRANSFER FLAVOPROTEIN or its dehydrogenase, electron transfer flavoprotein-ubiquinone oxidoreductase (EC 1.5.5.1).

Synonyms(22)

Synonym
Multiple FAD Dehydrogenase Deficiency
ETFDH Deficiency
Electron Transfer Flavoprotein Deficiency
Glutaric Acidemia Type II
Ethylmalonic-Adipic Aciduria
Electron Transfer Flavoprotein Beta Subunit Deficiency
ETFB Deficiency
Multiple Acyl Coenzyme A Dehydrogenase Deficiency
ETFA Deficiency
Multiple Acyl-CoA Dehydrogenase Deficiency
Glutaric Aciduria IIB
Ethylmalonic-Adipicaciduria
Glutaric Aciduria IIA
Glutaric Aciduria, Type 2
Electron Transfer Flavoprotein Dehydrogenase Deficiency
Electron Transfer Flavoprotein Alpha Subunit Deficiency
MADD (Multiple Acyl-CoA Dehydrogenase Deficiency)
Glutaric Aciduria Type II
Glutaric Acidemia, Type 2
Glutaric Aciduria IIC
Glutaric Aciduria Type 2
Glutaric Aciduria II

Research Excerpts

Overview

ExcerptReference
"ETFDH deficiency is a major cause of riboflavin-responsive MADD in southern China, and c."( Chen, XJ; Murong, SX; Wang, N; Wang, ZQ; Wu, ZY, 2011)
"Glutaric aciduria type II is a rare inborn error of metabolism."( Ceylaner, S; Işıkay, S; Yaman, A, 2017)

Context

ExcerptReference
"Late-onset glutaric aciduria type II has been described recently as a rare but treatable cause of proximal myopathy in teenagers and adults."( Hussain, S; Prasad, M, 2015)

Treatment

ExcerptReference
"Late-onset glutaric aciduria type II has been described recently as a rare but treatable cause of proximal myopathy in teenagers and adults."( Hussain, S; Prasad, M, 2015)

Research

Studies (118)

TimeframeStudies, This Condition (%)All Conditions %
pre-19900 (0.00)23.3326
1990's0 (0.00)12.5806
2000's9 (7.63)18.1394
2010's76 (64.41)28.8240
2020's33 (27.97)9.53
DrugIndicatedRelationship StrengthStudiesTrials
alpha-hydroxyglutarate0low30
gamma-aminobutyric acid0low10
carnitine0low330
3-hydroxybutyric acid0low30
methylmalonic acid0low10
creatine0low10
lactic acid0low10
glutaric acid0low40
nitrous oxide0low10
quinolinic acid0low10
succinic semialdehyde0low10
uric acid0low10
1-anilino-8-naphthalenesulfonate0low10
fentanyl0low10
metformin0low10
propofol0low10
triiodothyronine0low10
serine0low10
lysine0low10
adenosine monophosphate0low10
monomethyl succinate0low10
ethylmalonic acid0low40
glutamic acid0low10
s-adenosylmethionine0low220
bezafibrate0low20
6-hydroxy-2,5,7,8-tetramethylchroman-2-carboxylic acid0low10
adenosine0low10
valerates0low10
3-hydroxyglutaric acid0low20
2-ethylhydracrylic acid0low10
glycogen0low10
riboflavin0medium610
flavin-adenine dinucleotide0low100
coenzyme q100low110
topiramate0low10
selenium0low10
hypoglycin a0low20
palmitoylcarnitine0low10
ubiquinone0low150
guanine0low10

Protein Targets (612)

ProteinPotency MeasurementsInhibition MeasurementsActivation MeasurementsDrugs
Chain B, pheromone binding protein0011
Chain A, pheromone binding protein0011
Chain A, JmjC domain-containing histone demethylation protein 3A3003
Chain A, RNA-directed RNA polymerase NS50101
acid sphingomyelinase1001
thioredoxin reductase5005
USP1 protein, partial3003
TDP1 protein6006
vitamin D3 receptor isoform VDRA1001
importin subunit beta-1 isoform 12002
flap endonuclease 14004
serine/threonine-protein kinase PLK11001
snurportin-12002
peptidyl-prolyl cis-trans isomerase NIMA-interacting 13003
GTP-binding nuclear protein Ran isoform 12002
DNA polymerase eta isoform 11001
DNA polymerase iota isoform a (long)3003
urokinase-type plasminogen activator precursor1001
plasminogen precursor1001
urokinase plasminogen activator surface receptor precursor1001
geminin6006
DNA polymerase kappa isoform 12002
fibroblast growth factor 22 isoform 1 precursor0001
Mitogen-activated protein kinase 130101
Beta-lactamase0101
Transthyretin0012
Fatty acid-binding protein, intestinal0213
Fatty acid-binding protein, adipocyte0112
Cyclin-A20101
Cannabinoid receptor 10011
Cyclin-dependent kinase 20112
Choline O-acetyltransferase0202
Mitogen-activated protein kinase 120101
Guanine nucleotide-binding protein G2002
Fatty acid-binding protein 50011
Fatty acid-binding protein 50011
Mitogen-activated protein kinase 110101
Mitogen-activated protein kinase 140101
Protein skinhead-10101
Monocarboxylate transporter 20101
Solute carrier family 22 member 200202
Solute carrier family 22 member 60202
Solute carrier family 22 member 60204
Chain A, Beta-lactamase2002
GLS protein3003
euchromatic histone-lysine N-methyltransferase 28008
Polyphenol oxidase 20101
Acetylcholinesterase0101
Prostaglandin G/H synthase 10202
Sodium-dependent dopamine transporter0101
Prostaglandin G/H synthase 20101
Xanthine dehydrogenase/oxidase0101
Dehydrogenase/reductase SDR family member 90101
Chain A, MAJOR APURINIC/APYRIMIDINIC ENDONUCLEASE3003
Chain A, Membrane lipoprotein tmpC0011
Chain A, Membrane lipoprotein tmpC0011
Chain A, Membrane lipoprotein tmpC0011
Chain A, Structure of PAE2307 in complex with adenosine0011
Chain B, Structure of PAE2307 in complex with adenosine0011
Chain A, ADENOSINE RECEPTOR A2A0101
Chain A, ADENOSINE RECEPTOR A2A0101
Chain A, tRNA (guanine-N(1)-)-methyltransferase0011
Chain A, Uncharacterized protein MJ08830011
AR protein8008
signal transducer and activator of transcription 6, interleukin-4 induced1001
regulator of G-protein signaling 45005
glucocorticoid receptor [Homo sapiens]4004
retinoid X nuclear receptor alpha3003
estrogen nuclear receptor alpha110011
NPYLR7B0022
arylsulfatase A3003
IDH11001
Histone H2A.x2002
glycogen synthase kinase-3 beta isoform 10011
mitogen-activated protein kinase 12002
nuclear receptor ROR-gamma isoform 11001
peripheral myelin protein 224004
survival motor neuron protein isoform d2002
high affinity choline transporter 1 isoform a0101
Sodium/nucleoside cotransporter 10202
Calcium dependent protein kinase0101
Mitogen-activated protein kinase kinase kinase 70022
Sodium/nucleoside cotransporter 20202
Voltage-dependent calcium channel gamma-2 subunit1001
Rap guanine nucleotide exchange factor 31001
Purine nucleoside phosphorylase0303
Epidermal growth factor receptor0101
Phosphoglycerate kinase 1 0101
Adenosine deaminase0001
Avidin0011
Adenosine deaminase0001
Glyceraldehyde-3-phosphate dehydrogenase0202
Receptor tyrosine-protein kinase erbB-20101
Insulin receptor0001
Phosphoglycerate kinase 20101
Heat shock protein HSP 90-alpha0112
Platelet-derived growth factor receptor beta0001
Adenosine receptor A30225
Heat shock 70 kDa protein 1A 0101
Heat shock cognate 71 kDa protein0011
Fibroblast growth factor receptor 10001
Inosine-5'-monophosphate dehydrogenase 20101
Endoplasmin0112
Glutamate receptor 21315
Inosine-5'-monophosphate dehydrogenase 1 0101
Fibroblast growth factor receptor 20001
Fibroblast growth factor receptor 40001
Fibroblast growth factor receptor 30001
Streptavidin0011
Adenosylhomocysteinase0001
Adenosine receptor A10112
Adenosine receptor A30101
Adenosine receptor A2a0124
Adenosine receptor A2b0012
Adenosine receptor A2b0112
Adenylate kinase 2, mitochondrial0203
Adenosine receptor A10438
Adenosine receptor A2a0112
Adenylate kinase isoenzyme 1 0203
Phosphatidylinositol 4-kinase alpha0203
Adenosine receptor A10011
Adenosine kinase0001
Adenosine deaminase 0001
Equilibrative nucleoside transporter 20202
Phosphatidylinositol 4-kinase type 2-beta0203
Histone-lysine N-methyltransferase, H3 lysine-79 specific0101
Equilibrative nucleoside transporter 10202
Phosphatidylinositol 4-kinase type 2-alpha0203
Solute carrier family 28 member 30202
Adenosine kinase0102
Phosphatidylinositol 4-kinase beta0203
5-methylthioadenosine/S-adenosylhomocysteine deaminase0001
Adenosine transporter 10001
Chain A, Glycogen Phosphorylase B0011
Chain B, Glycogen Phosphorylase B0011
Chain A, ADP-dependent glucokinase0101
Chain A, Ribonuclease pancreatic0101
Chain A, Ribonuclease pancreatic0101
Chain A, phosphodiesterase-nucleotide pyrophosphatase0101
Chain A, GLYCOGEN PHOSPHORYLASE B0011
Chain B, GLYCOGEN PHOSPHORYLASE B0011
Chain A, GLYCOGEN PHOSPHORYLASE B0011
RAR-related orphan receptor gamma5005
estrogen-related nuclear receptor alpha6006
v-jun sarcoma virus 17 oncogene homolog (avian)4004
2'-deoxynucleoside 5'-phosphate N-hydrolase 10101
2'-deoxynucleoside 5'-phosphate N-hydrolase 10101
5'-AMP-activated protein kinase subunit beta-20011
Transient receptor potential cation channel subfamily M member 20101
Alcohol dehydrogenase E chain0101
Alcohol dehydrogenase S chain0101
L-lactate dehydrogenase A chain0112
Adenylate kinase isoenzyme 10001
Fructose-1,6-bisphosphatase 10101
Alkaline phosphatase, tissue-nonspecific isozyme0001
Fructose-1,6-bisphosphatase 10101
2-dehydropantoate 2-reductase0112
Inosine-5'-monophosphate dehydrogenase0101
Cytochrome P450 2C9 0101
Proto-oncogene tyrosine-protein kinase Src0101
Amine oxidase [flavin-containing] B0101
5'-nucleotidase0001
GTP:AMP phosphotransferase AK3, mitochondrial0001
P2Y purinoceptor 20011
P2Y purinoceptor 10011
P2Y purinoceptor 10011
5'-AMP-activated protein kinase subunit gamma-10022
5'-AMP-activated protein kinase catalytic subunit alpha-20011
Adenylate kinase 2, mitochondrial0001
Glycine--tRNA ligase0101
5'-AMP-activated protein kinase catalytic subunit alpha-10022
Adenosine deaminase-like protein0001
Protease 0112
P2Y purinoceptor 110011
Histamine H3 receptor0101
5'-AMP-activated protein kinase subunit gamma-30011
5'-AMP-activated protein kinase subunit gamma-20011
5'-AMP-activated protein kinase subunit beta-10022
ATP-dependent phosphofructokinase1001
Methylcytosine dioxygenase TET20112
Luciferase2002
phosphopantetheinyl transferase4004
aldehyde dehydrogenase 1 family, member A13003
farnesoid X nuclear receptor4004
pregnane X nuclear receptor6006
G2002
peroxisome proliferator-activated receptor delta2002
peroxisome proliferator activated receptor gamma3003
D(1A) dopamine receptor3003
chromobox protein homolog 13003
Glutamate receptor ionotropic, NMDA 2D0112
Glutamate receptor ionotropic, NMDA 3B0112
Bile salt export pump0101
5-hydroxytryptamine receptor 40213
Bile salt export pump0505
Interferon beta2002
HLA class I histocompatibility antigen, B alpha chain 2002
Fatty acid-binding protein, liver0101
Muscarinic acetylcholine receptor M10011
Muscarinic acetylcholine receptor M30011
Muscarinic acetylcholine receptor M40011
Muscarinic acetylcholine receptor M50011
Muscarinic acetylcholine receptor M20011
Peroxisome proliferator-activated receptor alpha0011
Peroxisome proliferator-activated receptor delta0011
Peroxisome proliferator-activated receptor gamma0033
Peroxisome proliferator-activated receptor gamma0011
Peroxisome proliferator-activated receptor delta0011
Glutamate receptor ionotropic, NMDA 10112
Peroxisome proliferator-activated receptor alpha0011
Glutamate receptor ionotropic, NMDA 2A0112
Glutamate receptor ionotropic, NMDA 2B0112
Glutamate receptor ionotropic, NMDA 2C0112
Glutamate receptor ionotropic, NMDA 3A0112
Inositol hexakisphosphate kinase 12002
cytochrome P450 2C9, partial2002
Solute carrier family 22 member 50001
Solute carrier family 22 member 50001
Solute carrier family 22 member 160001
Solute carrier family 22 member 210001
Solute carrier family 22 member 50001
lamin isoform A-delta105005
Sodium- and chloride-dependent creatine transporter 10101
Proton-coupled amino acid transporter 10404
cytochrome P450 family 3 subfamily A polypeptide 45005
potassium voltage-gated channel subfamily H member 2 isoform d2002
Solute carrier family 22 member 1 0202
Nuclear receptor subfamily 1 group I member 20011
ATP-dependent translocase ABCB10101
D(2) dopamine receptor0101
Amine oxidase [flavin-containing] A0101
D(4) dopamine receptor0101
Amine oxidase [flavin-containing] B0101
Delta-type opioid receptor0303
Delta-type opioid receptor0303
Mu-type opioid receptor0314
Kappa-type opioid receptor0101
Histamine H1 receptor0101
Mu-type opioid receptor0213
D(3) dopamine receptor0101
Delta-type opioid receptor0202
Kappa-type opioid receptor0202
Kappa-type opioid receptor0202
Mu-type opioid receptor0101
Mu-type opioid receptor0303
Potassium voltage-gated channel subfamily H member 20101
Sigma non-opioid intracellular receptor 10213
Sigma non-opioid intracellular receptor 10202
Sigma non-opioid intracellular receptor 10101
Chain A, Ferritin light chain3003
Gamma-aminobutyric acid 0011
Gamma-aminobutyric acid receptor subunit rho-30011
ATAD5 protein, partial1001
Hsf1 protein0011
thyroid stimulating hormone receptor3003
bromodomain adjacent to zinc finger domain 2B2002
Bloom syndrome protein isoform 13003
thyroid hormone receptor beta isoform a3003
transcriptional regulator ERG isoform 31001
histone-lysine N-methyltransferase 2A isoform 2 precursor1001
histone acetyltransferase KAT2A isoform 12002
neuropeptide S receptor isoform A3003
Gamma-aminobutyric acid receptor subunit pi0202
Gamma-aminobutyric acid receptor subunit pi3328
Gamma-aminobutyric acid receptor subunit delta0202
Histone deacetylase 30101
Gamma-aminobutyric acid type B receptor subunit 20011
Gamma-aminobutyric acid type B receptor subunit 20101
Gamma-aminobutyric acid receptor subunit alpha-10325
Gamma-aminobutyric acid receptor subunit beta-13328
Gamma-aminobutyric acid receptor subunit alpha-60011
Gamma-aminobutyric acid receptor subunit beta-10224
Gamma-aminobutyric acid receptor subunit delta3328
Gamma-aminobutyric acid receptor subunit gamma-20325
Gamma-aminobutyric acid receptor subunit gamma-23339
Gamma-aminobutyric acid receptor subunit alpha-53328
Gamma-aminobutyric acid receptor subunit alpha-33328
Gamma-aminobutyric acid receptor subunit gamma-20011
Gamma-aminobutyric acid receptor subunit delta0011
Gamma-aminobutyric acid receptor subunit gamma-13328
Gamma-aminobutyric acid receptor subunit alpha-23328
Sodium- and chloride-dependent GABA transporter 10202
Gamma-aminobutyric acid receptor subunit rho-10022
Gamma-aminobutyric acid receptor subunit alpha-20011
Gamma-aminobutyric acid receptor subunit alpha-30011
Gamma-aminobutyric acid receptor subunit gamma-30011
Gamma-aminobutyric acid receptor subunit alpha-43328
Gamma-aminobutyric acid receptor subunit beta-30325
Gamma-aminobutyric acid receptor subunit gamma-33328
Gamma-aminobutyric acid receptor subunit rho-20011
Gamma-aminobutyric acid receptor subunit alpha-63328
Sodium- and chloride-dependent GABA transporter 10101
Sodium- and chloride-dependent taurine transporter0101
Gamma-aminobutyric acid receptor subunit alpha-50224
Sodium- and chloride-dependent GABA transporter 20202
Sodium- and chloride-dependent GABA transporter 30202
Sodium- and chloride-dependent GABA transporter 10101
Sodium- and chloride-dependent GABA transporter 20202
Sodium- and chloride-dependent GABA transporter 30202
Gamma-aminobutyric acid receptor subunit alpha-30224
Gamma-aminobutyric acid receptor subunit alpha-20224
Gamma-aminobutyric acid receptor subunit beta-20224
Sodium- and chloride-dependent betaine transporter0202
Sodium- and chloride-dependent betaine transporter0101
Sodium- and chloride-dependent GABA transporter 30101
Gamma-aminobutyric acid receptor subunit alpha-40224
Gamma-aminobutyric acid receptor subunit beta-10011
Histone deacetylase 40101
Gamma-aminobutyric acid receptor subunit alpha-10011
Gamma-aminobutyric acid receptor subunit alpha-13339
Gamma-aminobutyric acid receptor subunit beta-33328
Gamma-aminobutyric acid receptor subunit beta-30011
Gamma-aminobutyric acid receptor subunit beta-23339
Gamma-aminobutyric acid receptor subunit epsilon0202
4-aminobutyrate aminotransferase, mitochondrial0001
4-aminobutyrate aminotransferase, mitochondrial0001
TAR DNA-binding protein 431001
Histone deacetylase 10101
Gamma-aminobutyric acid receptor subunit alpha-60224
Sterol O-acyltransferase 10011
Gamma-aminobutyric acid receptor subunit alpha-50011
Gamma-aminobutyric acid receptor subunit gamma-10202
Gamma-aminobutyric acid receptor subunit pi0011
Histone deacetylase 70101
GABA theta subunit3328
Histone deacetylase 20101
Polyamine deacetylase HDAC100101
Histone deacetylase 11 0101
Gamma-aminobutyric acid receptor subunit gamma-30202
Histone deacetylase 80101
Gamma-aminobutyric acid receptor subunit alpha-40011
Gamma-aminobutyric acid receptor subunit epsilon3328
Platelet glycoprotein VI0011
Gamma-aminobutyric acid receptor subunit theta0011
Sodium- and chloride-dependent GABA transporter 20101
Gamma-aminobutyric acid receptor subunit gamma-10011
Histone deacetylase 60101
Gamma-aminobutyric acid type B receptor subunit 10011
Histone deacetylase 90101
Gamma-aminobutyric acid receptor subunit theta0202
Histone deacetylase 50101
Gamma-aminobutyric acid type B receptor subunit 10101
Chain A, GLUTAMATE RECEPTOR SUBUNIT 20101
Chain A, Glutamate Receptor Subunit 20101
Chain B, Glutamate Receptor Subunit 20101
Chain A, Slr1257 protein0011
Chain A, Glucosamine--fructose-6-phosphate aminotransferase [isomerizing]0101
glp-1 receptor, partial2002
beta-2 adrenergic receptor1001
Metabotropic glutamate receptor 80202
Metabotropic glutamate receptor 60113
Excitatory amino acid transporter 40101
Glutathione reductase, mitochondrial0404
Bifunctional aspartokinase/homoserine dehydrogenase 10101
Prothrombin0022
Carbonic anhydrase 10305
Carbonic anhydrase 20316
Integrin beta-31012
Integrin alpha-IIb1012
ATP-citrate synthase 0101
Glutamate receptor 10314
Glutamate receptor 30314
Glutamate receptor 40314
Glutamate receptor ionotropic, kainate 10213
Metabotropic glutamate receptor 10112
Metabotropic glutamate receptor 20011
Metabotropic glutamate receptor 30011
Metabotropic glutamate receptor 40112
Metabotropic glutamate receptor 50011
Metabotropic glutamate receptor 60011
Metabotropic glutamate receptor 70011
Glutamate receptor ionotropic, NMDA 1 0527
Glutamate receptor ionotropic, kainate 10112
Metabotropic glutamate receptor 50113
Glutamate receptor ionotropic, kainate 20213
Glutamate receptor 10213
Glutamate receptor 20213
Glutamate receptor 30112
Glutamate receptor ionotropic, kainate 30202
Excitatory amino acid transporter 10203
Excitatory amino acid transporter 20203
Excitatory amino acid transporter 30203
Metabotropic glutamate receptor 80011
Glutamate receptor 40213
Excitatory amino acid transporter 3 0001
Glutamate racemase0001
Metabotropic glutamate receptor 80112
Fatty-acid amide hydrolase 10202
Glutamate receptor ionotropic, NMDA 2A 0527
Glutamate receptor ionotropic, NMDA 2B0628
Glutamate receptor ionotropic, NMDA 2C0527
Glutamate receptor ionotropic, kainate 40202
Glutamate carboxypeptidase 20101
Glutamate receptor ionotropic, kainate 20112
Glutamate receptor ionotropic, kainate 30101
Metabotropic glutamate receptor 10113
Metabotropic glutamate receptor 20113
Metabotropic glutamate receptor 70113
Metabotropic glutamate receptor 30113
Metabotropic glutamate receptor 40113
Glutamate receptor ionotropic, kainate 50101
Carbonic anhydrase-like protein, putative0001
Glutamate receptor ionotropic, NMDA 2D0527
Glutamate receptor ionotropic, kainate 50202
Glutamate racemase0001
Prolyl 4-hydroxylase0101
Glutamate receptor ionotropic, NMDA 3B0527
Alpha-ketoglutarate-dependent dioxygenase FTO0101
Glutamate receptor ionotropic, NMDA 3A0527
Chain A, Protein (aspartate Aminotransferase)0011
Chain A, Aspartate Aminotransferase0011
acetylcholinesterase3003
estrogen receptor 2 (ER beta)3003
nuclear receptor subfamily 1, group I, member 32002
retinoic acid nuclear receptor alpha variant 14004
thyroid hormone receptor beta isoform 23003
Solute carrier family 22 member 70001
Glycine receptor subunit alpha-10011
Sodium- and chloride-dependent glycine transporter 10101
Large neutral amino acids transporter small subunit 10101
Serine racemase0101
Olfactory receptor 51E20011
Sodium- and chloride-dependent glycine transporter 20202
Hypoxanthine-guanine phosphoribosyltransferase0001
Ricin0101
2-amino-4-hydroxy-6-hydroxymethyldihydropteridine pyrophosphokinase0011
Purine nucleoside phosphorylase 0012
Shiga toxin subunit A0101
Guanine deaminase0102
cytochrome P450 2D62002
thyroid stimulating hormone receptor2002
cellular tumor antigen p53 isoform a1001
Chain A, Ribulose-1,5 bisphosphate carboxylase/oxygenase large subunit N-methyltransferase, chloroplast0101
Chain A, Ribulose-1,5 bisphosphate carboxylase/oxygenase large subunit N-methyltransferase, chloroplast0101
Cationic amino acid transporter 30101
EWS/FLI fusion protein1001
cytochrome P450, family 19, subfamily A, polypeptide 1, isoform CRA_a3003
nuclear factor of kappa light polypeptide gene enhancer in B-cells 1 (p105), isoform CRA_a4004
Solute carrier family 22 member 20101
ATP-binding cassette sub-family C member 30202
Multidrug resistance-associated protein 40202
Dihydrofolate reductase0101
Dipeptidyl peptidase 40101
Solute carrier family 22 member 10001
Canalicular multispecific organic anion transporter 10202
Multidrug and toxin extrusion protein 10101
tumor susceptibility gene 101 protein1001
Serine racemase0101
N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase0101
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
GLI family zinc finger 31001
caspase 7, apoptosis-related cysteine protease1001
hypoxia-inducible factor 1, alpha subunit (basic helix-loop-helix transcription factor)1001
progesterone receptor3003
caspase-31001
activating transcription factor 62002
15-hydroxyprostaglandin dehydrogenase [NAD(+)] isoform 12002
heat shock protein beta-12002
cytochrome P450 3A4 isoform 13003
muscarinic acetylcholine receptor M12002
Fatty-acid amide hydrolase 10101
UDP-glucuronosyltransferase 1A90001
Cellular tumor antigen p533003
Aldo-keto reductase family 1 member B10202
Gamma-aminobutyric acid receptor subunit alpha-10001
Gamma-aminobutyric acid receptor subunit beta-10001
Gamma-aminobutyric acid receptor subunit alpha-20001
Gamma-aminobutyric acid receptor subunit alpha-30001
Polyunsaturated fatty acid lipoxygenase ALOX150101
Gamma-aminobutyric acid receptor subunit alpha-40001
Gamma-aminobutyric acid receptor subunit gamma-20001
Sodium-dependent noradrenaline transporter 0202
5-hydroxytryptamine receptor 2C0202
5-hydroxytryptamine receptor 2B0202
UDP-glucuronosyltransferase 1A80001
Chain A, Putative fructose-1,6-bisphosphate aldolase1001
Chain A, 2-oxoglutarate Oxygenase2002
15-lipoxygenase, partial2002
Microtubule-associated protein tau1001
Lysine-specific demethylase 4E0101
runt-related transcription factor 1 isoform AML1b1001
core-binding factor subunit beta isoform 21001
lethal(3)malignant brain tumor-like protein 1 isoform I1001
lethal factor (plasmid)3003
Advanced glycosylation end product-specific receptor0011
Beta-lactamase 0101
Advanced glycosylation end product-specific receptor0011
Chain A, TYROSYL-DNA PHOSPHODIESTERASE1001
Chain A, 6,7-Dimethyl-8-ribityllumazine Synthase0011
Chain B, 6,7-Dimethyl-8-ribityllumazine Synthase0011
Chain A, Breast cancer type 1 susceptibility protein1001
Chain H, Immunoglobulin Igg1 Heavy chain0011
Chain L, Immunoglobulin Igg1 Lambda Light Chain0011
Chain A, HADH2 protein1001
Chain B, HADH2 protein1001
Chain A, DODECIN0011
Chain A, DODECIN0011
Chain C, DODECIN0011
Chain E, DODECIN0011
Chain A, ATP-DEPENDENT DNA HELICASE Q11001
hypoxia-inducible factor 1 alpha subunit1001
SMAD family member 21001
SMAD family member 31001
vitamin D (1,25- dihydroxyvitamin D3) receptor1001
aryl hydrocarbon receptor2002
thyrotropin-releasing hormone receptor1001
tumor necrosis factor1001
nuclear factor NF-kappa-B p105 subunit isoform 11001
nuclear factor erythroid 2-related factor 2 isoform 12002
caspase-1 isoform alpha precursor1001
Riboflavin-binding protein0112
60 kDa chaperonin0101
60 kDa heat shock protein, mitochondrial0101
Caspase-71001
Spike glycoprotein1001
10 kDa heat shock protein, mitochondrial0101
Inositol monophosphatase 11001
Thiosulfate sulfurtransferase0101
60 kDa chaperonin 0101
10 kDa chaperonin 0101
Met repressor 0022
Protein arginine N-methyltransferase 50011
Histone H3K27 methylase0001
Phenylethanolamine N-methyltransferase0012
S-adenosylmethionine decarboxylase proenzyme0102
Protein-L-isoaspartate(D-aspartate) O-methyltransferase0101
Catechol O-methyltransferase0001
Protein arginine N-methyltransferase 10101
Methylosome protein 500011
Acetylcholinesterase0101
Pyruvate kinase PKM0011
Neutral amino acid transporter A0101
Cholinesterase0101
Neutral amino acid transporter B(0)0101
Amino acid transporter0101
Chain A, Carbonic anhydrase 10101
Carbonic anhydrase 0001
Carbonic anhydrase 0101
Carbonic anhydrase 0101
Carbonic anhydrase 0101
Carbonic anhydrase0101
Carbonic anhydrase0101
Carbonic anhydrase 120102
Prolyl endopeptidase0101
Carbonic anhydrase-related protein 110001
Sodium channel protein type 2 subunit alpha0101
Carbonic anhydrase 30101
Cytochrome P450 3A40101
Polyunsaturated fatty acid 5-lipoxygenase0101
Cytochrome P450 2C80101
Arachidonate 5-lipoxygenase-activating protein0101
Carbonic anhydrase 40102
Carbonic anhydrase 60102
Carbonic anhydrase 5A, mitochondrial0101
Carbonic anhydrase 20101
Cytochrome P450 2C190101
Carbonic anhydrase 5A, mitochondrial0113
Carbonic anhydrase0101
Carbonic anhydrase 70102
Carbonic anhydrase0101
D(2) dopamine receptor0101
Carbonic anhydrase 0101
Beta-carbonic anhydrase 10101
Carbonic anhydrase 20101
Neuronal acetylcholine receptor subunit alpha-70101
Carbonic anhydrase 90102
Carbonic anhydrase, alpha family 0101
Carbonic anhydrase 0101
Carbonic anhydrase0101
Carbonic anhydrase0101
Carbonic anhydrase 0101
Delta carbonic anhydrase0101
Carbonic anhydrase 0101
Carbonic anhydrase 130101
Carbonic anhydrase 40202
Carbonic anhydrase 150101
Carbonic anhydrase 130102
Carbonic anhydrase 140102
Carbonic anhydrase 5B, mitochondrial0102
Chain X, Thyroid hormone receptor beta-10011
Chain X, Thyroid hormone receptor beta-10011
apical membrane antigen 1, AMA11001
glucocerebrosidase1001
muscleblind-like protein 1 isoform 11001
Solute carrier organic anion transporter family member 1A40102
Solute carrier organic anion transporter family member 1A50001
Androgen receptor0101
Thyroid hormone receptor alpha0224
Thyroid hormone receptor beta0224
Proliferating cell nuclear antigen0101
Thyroid hormone receptor beta0101
Solute carrier organic anion transporter family member 1A20001
Solute carrier organic anion transporter family member 1A30001
Solute carrier organic anion transporter family member 4C10001
Solute carrier organic anion transporter family member 4C10001
Solute carrier organic anion transporter family member 4A10001
Solute carrier organic anion transporter family member 1C10101
Solute carrier organic anion transporter family member 1B30001
Solute carrier organic anion transporter family member 1B10001
Chain A, Glycogen phosphorylase, liver form0011
Chain A, glycogen phosphorylase, liver form0011
Chain A, Glycogen phosphorylase, liver form0011
Chain A, Glycogen phosphorylase, liver form0011
Solute carrier family 22 member 80101
Solute carrier family 2, facilitated glucose transporter member 90112
Carbonic anhydrase0101
[prepared from compound, protein, and bioassay information from National Library of Medicine (NLM), extracted Dec-2023]