Page last updated: 2024-09-28

Beckwith-Wiedemann Syndrome

A syndrome of multiple defects characterized primarily by umbilical hernia (HERNIA, UMBILICAL); MACROGLOSSIA; and GIGANTISM; and secondarily by visceromegaly; HYPOGLYCEMIA; and ear abnormalities.

Synonyms(6)

Synonym
EMG Syndrome
Beckwith-Wiedemann Syndrome
Wiedemann-Beckwith Syndrome (WBS)
Wiedemann Syndrome
Wiedemann-Beckwith Syndrome
Exomphalos-Macroglossia-Gigantism Syndrome

Research Excerpts

Overview

ExcerptReference
"Beckwith-Wiedemann syndrome is a rare condition (1/13,700 live births) occurring in both inherited and sporadic forms in the population."( Grant, D; Nystrom, A; Schofield, PN; Smith, J; Spitz, L; Zapf, J, 1995)
"Beckwith-Wiedemann syndrome is a congenital disorder manifested by organomegaly, omphalocele, hypoglycemia, and macroglossia."( Kenna, MA; Rimell, FL; Shapiro, AM; Shoemaker, DL, 1995)
"Beckwith-Wiedemann syndrome is a congenital syndrome with some anomaly in overgrowth."( Karaman, E; Kaytaz, A; Mercan, H; Yilmaz, M, 2009)

Research

Studies (99)

TimeframeStudies, This Condition (%)All Conditions %
pre-199010 (10.10)23.3326
1990's25 (25.25)12.5806
2000's28 (28.28)18.1394
2010's30 (30.30)28.8240
2020's6 (6.06)9.53
DrugIndicatedRelationship StrengthStudiesTrials
carnitine0low10
salicylic acid0low10
cytosine0low10
methanol0low10
nitrous oxide0low10
sulfites0low10
acetaminophen0low10
chloroquine0low10
clonazepam0low10
diazoxide0low50
valproic acid0low10
fentanyl0low40
halothane0low20
hydrochlorothiazide0low10
2-propanol0low30
midazolam0low10
mitotane0low10
apnea0low10
ofloxacin0low10
propofol0low20
propranolol0low10
sevoflurane0low10
succinylcholine0low10
tetracaine0low10
thalidomide0low10
prednisone0low10
dehydroepiandrosterone0low10
lysine0low10
tyrosine0low10
androstenedione0low10
methionine0low20
17-alpha-hydroxyprogesterone0low10
methylprednisolone0low10
azacitidine0low30
acetylcysteine0low10
dehydroepiandrosterone sulfate0low10
camptothecin0low10
sodium sulfate0low10
irinotecan0low10
cephalosporin c0low10
fluorodeoxyglucose f180low10
hydrogen sulfite0low10
atropine0low10
glycogen0low30
elastin0low10
inositol 3-phosphate0medium11
cortodoxone0low10
quinidine0low10
pancuronium0low10
tacrolimus0low10
mycophenolic acid0low20
decitabine0low20
dactinomycin0low20
isomethyleugenol0low180
sirolimus0low10
ribose0low10
cefdinir0low10
atrial natriuretic factor0low10
glucagon0low20
liraglutide0low10
vendex0medium11
natriuretic peptide, brain0low10
heparitin sulfate0low40
ascorbic acid0low10
tetracycline0low10
transforming growth factor beta0low10
folic acid0low10
sildenafil citrate0low10
cytidylyl-3'-5'-guanosine0low40

Protein Targets (1,022)

ProteinPotency MeasurementsInhibition MeasurementsActivation MeasurementsDrugs
acetylcholinesterase7007
pregnane X receptor6006
SMAD family member 25005
SMAD family member 35005
TDP1 protein220022
GLI family zinc finger 3180018
Microtubule-associated protein tau6006
AR protein210021
progesterone receptor140014
glucocorticoid receptor [Homo sapiens]210021
retinoic acid nuclear receptor alpha variant 1160016
retinoid X nuclear receptor alpha180018
estrogen-related nuclear receptor alpha220022
farnesoid X nuclear receptor120012
pregnane X nuclear receptor130013
estrogen nuclear receptor alpha280028
G6006
vitamin D (1,25- dihydroxyvitamin D3) receptor130013
arylsulfatase A110011
euchromatic histone-lysine N-methyltransferase 2210021
cytochrome P450, family 19, subfamily A, polypeptide 1, isoform CRA_a140014
activating transcription factor 68008
nuclear receptor subfamily 1, group I, member 23003
chromobox protein homolog 1100010
nuclear factor erythroid 2-related factor 2 isoform 1150015
geminin190019
survival motor neuron protein isoform d100010
histone acetyltransferase KAT2A isoform 18008
lamin isoform A-delta10150015
Voltage-dependent calcium channel gamma-2 subunit7007
Interferon beta110011
HLA class I histocompatibility antigen, B alpha chain 6006
Glucocorticoid receptor0617
Sex hormone-binding globulin0044
Glycine receptor subunit alpha-10606
Corticosteroid-binding globulin0404
Adenosine receptor A30617
Replicase polyprotein 1ab0213
Androgen receptor0505
Alpha-1B adrenergic receptor0617
Glutamate receptor 271010
Glycine receptor subunit beta0606
Glycine receptor subunit alpha-20606
Glycine receptor subunit alpha-30606
Mitogen-activated protein kinase 3 0112
Alpha-1A adrenergic receptor0617
Sodium-dependent dopamine transporter 0404
TAR DNA-binding protein 434004
Inositol hexakisphosphate kinase 16006
cytochrome P450 2C9, partial6006
ATP-dependent phosphofructokinase6006
hypoxia-inducible factor 1 alpha subunit5005
RAR-related orphan receptor gamma150015
aldehyde dehydrogenase 1 family, member A1160016
peroxisome proliferator-activated receptor delta7007
v-jun sarcoma virus 17 oncogene homolog (avian)6006
Histone H2A.x8008
thyroid hormone receptor beta isoform a8008
heat shock protein beta-15005
ATAD5 protein, partial8008
GLS protein4004
Smad34004
thyroid stimulating hormone receptor8008
nuclear receptor subfamily 1, group I, member 3130013
EWS/FLI fusion protein8008
peroxisome proliferator activated receptor gamma120012
aryl hydrocarbon receptor6006
thyroid hormone receptor beta isoform 2160016
peripheral myelin protein 22100010
cytochrome P450 3A4 isoform 19009
Gamma-aminobutyric acid receptor subunit pi95216
ATP-binding cassette sub-family C member 3014014
Multidrug resistance-associated protein 4015017
Solute carrier family 22 member 60404
Carbonic anhydrase 120305
UDP-glucuronosyltransferase 1A90004
Bile salt export pump0404
Bile salt export pump023023
Cytochrome P450 2B10001
Cytochrome P450 1A10001
Carbonic anhydrase 10709
Carbonic anhydrase 208010
Myoglobin0101
Cytochrome P450 1A10012
Cytochrome P450 1A20102
Prostaglandin G/H synthase 10202
Carbonic anhydrase 30305
Cytochrome P450 3A40808
Cytochrome P450 2D60404
Cytochrome P450 2C9 0505
Polyunsaturated fatty acid lipoxygenase ALOX150202
Gamma-aminobutyric acid receptor subunit beta-195216
Sulfotransferase 1A1 0001
Gamma-aminobutyric acid receptor subunit delta95216
Gamma-aminobutyric acid receptor subunit gamma-295216
UDP-glucuronosyltransferase 1-60204
Gamma-aminobutyric acid receptor subunit alpha-595216
Gamma-aminobutyric acid receptor subunit alpha-395216
Arachidonate 5-lipoxygenase-activating protein0101
UDP-glucuronosyltransferase 1A1 0204
Carbonic anhydrase 40507
Prostaglandin G/H synthase 10303
Carbonic anhydrase 60305
Gamma-aminobutyric acid receptor subunit gamma-195216
Gamma-aminobutyric acid receptor subunit alpha-295216
Gamma-aminobutyric acid receptor subunit alpha-495216
Gamma-aminobutyric acid receptor subunit gamma-395216
Gamma-aminobutyric acid receptor subunit alpha-695216
Carbonic anhydrase 5A, mitochondrial0406
Prostaglandin G/H synthase 20102
Carbonic anhydrase 70305
Nuclear receptor ROR-gamma8008
Cytochrome P450 2J20303
Gamma-aminobutyric acid receptor subunit alpha-195216
Gamma-aminobutyric acid receptor subunit beta-395216
Gamma-aminobutyric acid receptor subunit beta-295216
Carbonic anhydrase 90305
GABA theta subunit95216
Canalicular multispecific organic anion transporter 1014014
Carbonic anhydrase 150304
Carbonic anhydrase 130304
Gamma-aminobutyric acid receptor subunit epsilon95216
Carbonic anhydrase 140305
Carbonic anhydrase 5B, mitochondrial0305
toxin B0001
Chain A, JmjC domain-containing histone demethylation protein 3A2002
Chain A, 2-oxoglutarate Oxygenase9009
Chain A, ATP-DEPENDENT DNA HELICASE Q12002
dopamine D1 receptor1001
15-lipoxygenase, partial3003
phosphopantetheinyl transferase4004
USP1 protein, partial6006
NFKB1 protein, partial3003
Thrombopoietin3003
regulator of G-protein signaling 45005
Bloom syndrome protein isoform 1100010
D(1A) dopamine receptor6006
flap endonuclease 13003
muscarinic acetylcholine receptor M17007
Histone deacetylase 30404
Histone deacetylase 40404
Guanine nucleotide-binding protein G2002
Histone deacetylase 10404
Histone deacetylase 70404
Histone deacetylase 20404
Polyamine deacetylase HDAC100404
Histone deacetylase 11 0404
Ataxin-2100010
Histone deacetylase 80404
Histone deacetylase 60404
Histone deacetylase 90404
Histone deacetylase 50404
Chain A, HADH2 protein9009
Chain B, HADH2 protein9009
interleukin 83003
estrogen receptor 2 (ER beta)7007
cytochrome P450 family 3 subfamily A polypeptide 4100010
nonstructural protein 12002
Caspase-73003
peripheral myelin protein 22 isoform 15005
potassium voltage-gated channel subfamily H member 2 isoform d8008
caspase-33003
importin subunit beta-1 isoform 12002
mitogen-activated protein kinase 13003
nuclear factor NF-kappa-B p105 subunit isoform 12002
snurportin-12002
GTP-binding nuclear protein Ran isoform 12002
DNA polymerase iota isoform a (long)3003
nuclear receptor ROR-gamma isoform 17007
muscleblind-like protein 1 isoform 13003
neuropeptide S receptor isoform A2002
Beta-glucuronidase0202
Cholinesterase0202
Aromatase0204
Gastrin/cholecystokinin type B receptor0102
Testosterone 17-beta-dehydrogenase 30101
Alpha-synuclein4206
thioredoxin reductase110011
Chain A, Hyaluronidase, phage associated0101
thioredoxin glutathione reductase2002
IDH14004
nuclear factor erythroid 2-related factor 2 isoform 2100010
lethal(3)malignant brain tumor-like protein 1 isoform I2002
lethal factor (plasmid)6006
Polyphenol oxidase 20204
Pancreatic alpha-amylase0202
Albumin0101
Urease0101
Prolyl 4-hydroxylase subunit alpha-10001
Tyrosinase0101
Alpha-2B adrenergic receptor0124
Spike glycoprotein81110
Hyaluronate lyase0101
Prolyl hydroxylase EGLN20001
Egl nine homolog 10001
Prolyl hydroxylase EGLN30001
Hypoxia-inducible factor 1-alpha inhibitor0001
Solute carrier family 23 member 10101
Atrial natriuretic peptide receptor 10112
Atrial natriuretic peptide receptor 1 0011
cystic fibrosis transmembrane conductance regulator0101
DNA polymerase beta2002
short transient receptor potential channel 6 isoform 10011
Solute carrier family 22 member 1 0708
5-hydroxytryptamine receptor 40808
Muscarinic acetylcholine receptor M205210
Muscarinic acetylcholine receptor M40518
Muscarinic acetylcholine receptor M10215
Muscarinic acetylcholine receptor M30215
Muscarinic acetylcholine receptor M40215
Muscarinic acetylcholine receptor M50215
Muscarinic acetylcholine receptor M50316
Muscarinic acetylcholine receptor M20216
Muscarinic acetylcholine receptor M10429
Muscarinic acetylcholine receptor M10001
Muscarinic acetylcholine receptor M30428
Alpha-1D adrenergic receptor0214
5-hydroxytryptamine receptor 2C0819
Muscarinic acetylcholine receptor M40101
Histamine H2 receptor1002
5-hydroxytryptamine receptor 70303
Reverse transcriptase/RNaseH 0102
Muscarinic acetylcholine receptor0112
Chain A, MAJOR APURINIC/APYRIMIDINIC ENDONUCLEASE6006
Chain A, Beta-lactamase4004
glp-1 receptor, partial5005
Fumarate hydratase4004
PPM1D protein6006
polyprotein4004
67.9K protein6006
Parkin1001
thyroid stimulating hormone receptor4004
hemoglobin subunit beta2002
cellular tumor antigen p53 isoform a2002
huntingtin isoform 23003
ras-related protein Rab-9A2002
serine/threonine-protein kinase mTOR isoform 13003
urokinase-type plasminogen activator precursor3003
plasminogen precursor3003
urokinase plasminogen activator surface receptor precursor3003
Cellular tumor antigen p53120012
Integrin beta-32002
Integrin alpha-IIb2002
DNA (cytosine-5)-methyltransferase 10202
Adenosine receptor A2a0213
Adenosine receptor A10101
D(1A) dopamine receptor2002
Multidrug and toxin extrusion protein 10303
Histone-lysine N-methyltransferase EHMT20202
ATPase family AAA domain-containing protein 57007
Chain A, Ferritin light chain7007
Chain A, Cruzipain3003
DNA topoisomerase 0101
hypoxia-inducible factor 1, alpha subunit (basic helix-loop-helix transcription factor)6006
glucocerebrosidase2002
putative alpha-glucosidase1001
alpha-galactosidase2002
lysosomal alpha-glucosidase preproprotein2002
cytochrome P450 2C19 precursor1001
15-hydroxyprostaglandin dehydrogenase [NAD(+)] isoform 16006
eukaryotic translation initiation factor 2-alpha kinase 3 isoform 1 precursor0011
M-phase phosphoprotein 82002
relaxin receptor 1 isoform 11001
Telomerase reverse transcriptase0101
Serine/threonine-protein kinase Chk10022
Type-2 restriction enzyme ScaI0101
Deoxyribonuclease-2-alpha0101
Tyrosyl-DNA phosphodiesterase 20101
Deoxyribonuclease-10101
Type-2 restriction enzyme PstI0101
Type-2 restriction enzyme EcoRI0101
Prothrombin0001
DNA ligase0202
Heterogeneous nuclear ribonucleoprotein A10011
DNA topoisomerase 10117
DNA topoisomerase 2-alpha0112
Type-2 restriction enzyme BamHI0101
Somatostatin receptor type 10101
Somatostatin receptor type 20101
Somatostatin receptor type 40101
Somatostatin receptor type 30101
Somatostatin receptor type 50101
5-hydroxytryptamine receptor 2B0819
Type-2 restriction enzyme HindIII0101
Ribonuclease pancreatic0101
Inositol monophosphatase 11001
DNA topoisomerase 2-beta0012
DNA topoisomerase 10102
DNA topoisomerase 10101
Integrase 0202
DNA topoisomerase type IB small subunit 0011
Tyrosyl-DNA phosphodiesterase 10101
Solute carrier family 22 member 50001
Solute carrier family 22 member 50001
Solute carrier family 22 member 160001
Solute carrier family 22 member 210001
Solute carrier family 22 member 50001
glucose-6-phosphate dehydrogenase-6-phosphogluconolactonase0101
Spike glycoprotein0112
Replicase polyprotein 1ab0112
glucose-6-phosphate 1-dehydrogenase isoform b0101
Transmembrane protease serine 20112
Dihydrofolate reductase 0101
Riboflavin-binding protein0011
Major prion protein0011
Amyloid-beta precursor protein0101
Histidine-rich protein PFHRP-II0203
Procathepsin L0112
Alpha-2A adrenergic receptor0427
Replicase polyprotein 1a0112
Replicase polyprotein 1ab0112
Replicase polyprotein 1ab0112
Spike glycoprotein0101
Ribosyldihydronicotinamide dehydrogenase [quinone]0112
Alpha-2C adrenergic receptor0427
DNA ligase 10101
Serine/threonine-protein kinase mTOR0314
Nuclear receptor subfamily 4 group A member 20011
Beta-secretase 10101
Calcium-dependent protein kinase 10011
MO15-related protein kinase Pfmrk 0101
DNA ligase A0101
Potassium voltage-gated channel subfamily H member 20606
Sigma intracellular receptor 20101
Phosphoethanolamine N-methyltransferase0101
Sigma non-opioid intracellular receptor 10707
Angiotensin-converting enzyme 2 0112
Cysteine proteinase falcipain 2a 0101
Cysteine proteinase falcipain 2a 0101
Gamma-aminobutyric acid receptor subunit pi0202
Gamma-aminobutyric acid receptor subunit delta0202
Gamma-aminobutyric acid receptor subunit alpha-10102
Gamma-aminobutyric acid receptor subunit beta-10102
Neuronal acetylcholine receptor subunit alpha-40101
Gamma-aminobutyric acid receptor subunit alpha-20102
Gamma-aminobutyric acid receptor subunit alpha-30102
Neuronal acetylcholine receptor subunit beta-20101
Gamma-aminobutyric acid receptor subunit alpha-10314
Gamma-aminobutyric acid receptor subunit beta-10213
Gamma-aminobutyric acid receptor subunit gamma-20314
Gamma-aminobutyric acid receptor subunit alpha-40102
Gamma-aminobutyric acid receptor subunit gamma-20102
Gamma-aminobutyric acid receptor subunit beta-30314
Translocator protein0101
Translocator protein0101
Cholecystokinin receptor type A0101
Gamma-aminobutyric acid receptor subunit alpha-50213
Gamma-aminobutyric acid receptor subunit alpha-30213
Gamma-aminobutyric acid receptor subunit alpha-20213
Gamma-aminobutyric acid receptor subunit beta-20213
Gamma-aminobutyric acid receptor subunit alpha-40213
Gamma-aminobutyric acid receptor subunit epsilon0202
Gamma-aminobutyric acid receptor subunit alpha-60213
Gamma-aminobutyric acid receptor subunit gamma-10202
Gamma-aminobutyric acid receptor subunit gamma-30202
Gamma-aminobutyric acid receptor subunit theta0202
endonuclease IV1001
bromodomain adjacent to zinc finger domain 2B3003
Deoxycytidine kinase0001
Chain A, Putative fructose-1,6-bisphosphate aldolase2002
caspase 7, apoptosis-related cysteine protease2002
caspase-32002
RAD510101
vitamin D3 receptor isoform VDRA3003
histone-lysine N-methyltransferase 2A isoform 2 precursor1001
caspase-1 isoform alpha precursor1001
ATP-dependent translocase ABCB10709
Dolichyl-diphosphooligosaccharide--protein glycosyltransferase subunit 10101
Caspase-71001
Growth factor receptor-bound protein 20101
Pantothenate synthetase0101
Discoidin domain-containing receptor 20112
Growth factor receptor-bound protein 2 0101
Peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase0011
exodeoxyribonuclease V subunit RecD0101
exodeoxyribonuclease V subunit RecB0101
exodeoxyribonuclease V subunit RecC0101
cytochrome P450 2D63003
Beta-glucuronidase0101
Glucose-6-phosphate 1-dehydrogenase0202
G-protein coupled bile acid receptor 10022
Glucose-6-phosphate 1-dehydrogenase 0101
NPC1-like intracellular cholesterol transporter 10011
Solute carrier organic anion transporter family member 1A40102
Solute carrier organic anion transporter family member 1A50001
Steryl-sulfatase0001
Multidrug resistance-associated protein 1 0001
Solute carrier organic anion transporter family member 1A10102
Solute carrier organic anion transporter family member 1A20001
Solute carrier organic anion transporter family member 1A30102
ATP-binding cassette sub-family C member 110001
Solute carrier organic anion transporter family member 1B30001
Solute carrier family 22 member 110002
Solute carrier organic anion transporter family member 1A10001
Solute carrier organic anion transporter family member 1B20001
Solute carrier organic anion transporter family member 1B10203
cytochrome P450 2D6 isoform 11001
Coagulation factor VII0101
Tissue factor0202
Glutamate receptor 10103
Glutamate receptor 30103
Glutamate receptor 40103
Nicotinamide phosphoribosyltransferase0011
ATP-binding cassette sub-family C member 80112
ATP-sensitive inward rectifier potassium channel 110112
Luciferase2002
Nuclear receptor subfamily 1 group I member 20044
D(2) dopamine receptor0213
Amine oxidase [flavin-containing] A0202
D(4) dopamine receptor0101
Amine oxidase [flavin-containing] B0101
Delta-type opioid receptor0303
Delta-type opioid receptor0303
Mu-type opioid receptor0415
Kappa-type opioid receptor0101
Histamine H1 receptor0101
Mu-type opioid receptor0325
D(3) dopamine receptor0101
Delta-type opioid receptor0314
Kappa-type opioid receptor0202
Kappa-type opioid receptor0314
Mu-type opioid receptor0101
Mu-type opioid receptor0303
Sigma non-opioid intracellular receptor 10303
Sigma non-opioid intracellular receptor 10101
Chain A, TYROSYL-DNA PHOSPHODIESTERASE5005
Chain A, Dihydrofolate reductase0011
acid sphingomyelinase1001
Thymidylate synthase0202
Thymidylate synthase0101
Dihydrofolate reductase0011
Aldo-keto reductase family 1 member B10202
Folylpolyglutamate synthase, mitochondrial0001
Folylpolyglutamate synthase, mitochondrial0001
Multidrug resistance associated protein0001
Albumin0325
Voltage-dependent L-type calcium channel subunit alpha-1C0303
Carbonic anhydrase 0202
Hsf1 protein0011
Carbonic anhydrase 0101
cytochrome P450 2C9 precursor1001
Carbonic anhydrase, alpha family 0101
Carbonic anhydrase 0101
Delta carbonic anhydrase0101
Carbonic anhydrase0203
Chain A, Acetylcholinesterase0101
interferon gamma precursor0001
Solute carrier family 22 member 20101
Solute carrier family 22 member 30101
Interstitial collagenase0101
Acetylcholinesterase0101
Acetylcholinesterase0303
Liver carboxylesterase 10102
Multidrug and toxin extrusion protein 20101
Glucagon-like peptide 1 receptor0224
Chain A, Ribulose-1,5 bisphosphate carboxylase/oxygenase large subunit N-methyltransferase, chloroplast0101
Chain A, Ribulose-1,5 bisphosphate carboxylase/oxygenase large subunit N-methyltransferase, chloroplast0101
Glutathione reductase, mitochondrial0202
Cationic amino acid transporter 30101
Chain A, Methionyl-tRNA synthetase0011
Chain A, Methionyl-tRNA synthetase0011
Chain A, Aminopeptidase0101
Chain A, Methionine aminopeptidase0101
S-ribosylhomocysteine lyase0101
Adenylate cyclase type 50001
S-adenosylmethionine synthase isoform type-10001
S-adenosylmethionine synthase isoform type-20001
Fatty acid synthase0101
Large neutral amino acids transporter small subunit 10202
Nuclear receptor subfamily 1 group I member 20011
ATP-dependent translocase ABCB10202
Translocator protein0101
UDP-glucuronosyltransferase 2B70305
ATP-dependent translocase ABCB10202
UDP-glucuronosyltransferase 1A40203
UDP-glucuronosyltransferase 2B10 0202
nuclear factor of kappa light polypeptide gene enhancer in B-cells 1 (p105), isoform CRA_a3003
serine-protein kinase ATM isoform a1001
parathyroid hormone/parathyroid hormone-related peptide receptor precursor2002
peptidyl-prolyl cis-trans isomerase NIMA-interacting 11001
Aldo-keto reductase family 1 member B10505
Sodium-dependent noradrenaline transporter 0404
Sodium-dependent serotonin transporter0404
5-hydroxytryptamine receptor 60415
Peroxisome proliferator-activated receptor alpha1001
Rap guanine nucleotide exchange factor 41001
Chain A, Inosine-5'-Monophosphate Dehydrogenase 20101
Inosine-5'-monophosphate dehydrogenase 20213
Inosine-5'-monophosphate dehydrogenase 1 0202
Sodium-dependent serotonin transporter0101
Peroxisome proliferator-activated receptor gamma0011
Inosine-5'-monophosphate dehydrogenase0102
UDP-glucuronosyltransferase 1A70001
UDP-glucuronosyltransferase 1A100001
UDP-glucuronosyltransferase 1A80002
STE240001
CAAX prenyl protease0001
streptokinase A precursor0011
Trypsin0001
DNA gyrase subunit A0102
DNA gyrase subunit B0102
DNA gyrase subunit B0102
DNA gyrase subunit A0102
Glutamate 5-kinase0001
Angiotensin-converting enzyme 0101
Glutamate receptor ionotropic, NMDA 1 0102
Neutral amino acid transporter A0202
Neutral amino acid transporter B(0)0202
Proton-coupled amino acid transporter 10202
Amino acid transporter0202
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
Chain A, Ferritin light chain0011
Fatty-acid amide hydrolase 10101
Sodium- and chloride-dependent GABA transporter 10101
Sodium- and chloride-dependent GABA transporter 20101
Sodium- and chloride-dependent GABA transporter 30101
Sodium- and chloride-dependent betaine transporter0101
Fatty-acid amide hydrolase 10101
Beta-1 adrenergic receptor 0113
Voltage-dependent L-type calcium channel subunit alpha-1C0202
Beta-2 adrenergic receptor0213
Beta-1 adrenergic receptor0213
5-hydroxytryptamine receptor 1A0101
Beta-2 adrenergic receptor0203
Cytochrome P450 2C80101
Beta-3 adrenergic receptor0213
Beta-1 adrenergic receptor0214
D(3) dopamine receptor0101
5-hydroxytryptamine receptor 1A0214
Alpha-2B adrenergic receptor0011
D(1A) dopamine receptor0112
Voltage-dependent L-type calcium channel subunit alpha-1C0101
Alpha-2C adrenergic receptor0011
Alpha-2A adrenergic receptor0011
Alpha-1D adrenergic receptor0213
Endothelin-1 receptor0112
Beta-3 adrenergic receptor0202
5-hydroxytryptamine receptor 1B0213
5-hydroxytryptamine receptor 2A0415
5-hydroxytryptamine receptor 1B0202
Neuromedin-K receptor0011
Type-1 angiotensin II receptor0112
Cholecystokinin receptor type A0112
Cytochrome P450 2C190202
5-hydroxytryptamine receptor 70112
Beta-1 adrenergic receptor0101
Alpha-1A adrenergic receptor0124
Alpha-1B adrenergic receptor0012
Vasopressin V1a receptor0112
Beta-2 adrenergic receptor0101
Sodium channel protein type 5 subunit alpha0303
Sodium/bile acid cotransporter0101
Beta-2 adrenergic receptor0113
Nuclear receptor subfamily 2 group E member 10022
Voltage-dependent L-type calcium channel subunit alpha-1F0101
Cytochrome P450 2D10101
Cytochrome P450 2D260101
Cytochrome P450 2D30101
Potassium voltage-gated channel subfamily A member 50101
Cholinesterase0202
Voltage-dependent L-type calcium channel subunit alpha-1D 0101
Voltage-dependent L-type calcium channel subunit alpha-1S0101
Solute carrier family 22 member 10203
Potassium voltage-gated channel subfamily D member 20101
Cytochrome P450 2D40101
Multidrug resistance protein 1a0001
Solute carrier family 22 member 20202
chaperonin-containing TCP-1 beta subunit homolog1001
Estrogen receptor beta0001
Inhibitor of nuclear factor kappa-B kinase subunit beta0001
5'-AMP-activated protein kinase subunit beta-20001
Polymerase acidic protein0011
Stromelysin-10112
Tyrosine-protein phosphatase YopH0101
High mobility group protein B10011
Prolyl 4-hydroxylase subunit alpha-10101
Tyrosine-protein phosphatase non-receptor type 10103
Estrogen receptor0001
Cystathionine gamma-lyase0101
5'-AMP-activated protein kinase subunit gamma-10012
5'-AMP-activated protein kinase catalytic subunit alpha-20001
Xanthine dehydrogenase/oxidase0101
5'-AMP-activated protein kinase catalytic subunit alpha-10012
Carbonic anhydrase0101
Solute carrier family 22 member 60101
Solute carrier family 22 member 70001
Nicotinate phosphoribosyltransferase0101
Solute carrier family 22 member 200101
Solute carrier family 22 member 80102
Solute carrier family 22 member 60101
Ubiquitin-like domain-containing CTD phosphatase 10101
5'-AMP-activated protein kinase subunit gamma-30001
5'-AMP-activated protein kinase subunit gamma-20012
5'-AMP-activated protein kinase subunit beta-10001
DNA polymerase kappa isoform 13003
Acetylcholinesterase0101
Pyruvate kinase PKM0011
cGMP-specific 3',5'-cyclic phosphodiesterase0101
Bone morphogenetic protein receptor type-1B0011
Cell division cycle 7-related protein kinase0011
Serine/threonine-protein kinase PLK40011
ATP-dependent RNA helicase DDX3X0011
Pyridoxal kinase0011
Citron Rho-interacting kinase0011
Aurora kinase A0011
Cyclin-G-associated kinase0011
Ephrin type-B receptor 60011
Peroxisomal acyl-coenzyme A oxidase 30011
Receptor-interacting serine/threonine-protein kinase 20011
Mitotic checkpoint serine/threonine-protein kinase BUB10011
Dynamin-like 120 kDa protein, mitochondrial0011
Tyrosine-protein kinase JAK20011
Eukaryotic translation initiation factor 5B0011
Rho-associated protein kinase 20011
Serine/threonine-protein kinase ULK10011
Serine/threonine-protein kinase/endoribonuclease IRE10011
Ribosomal protein S6 kinase alpha-50011
U5 small nuclear ribonucleoprotein 200 kDa helicase0011
Ribosomal protein S6 kinase alpha-40011
Serine/threonine-protein kinase 160011
Cyclin-dependent kinase-like 50011
Serine/threonine-protein kinase 100011
Serine/threonine-protein kinase D30011
Structural maintenance of chromosomes protein 20011
Mitogen-activated protein kinase kinase kinase 60011
Mitogen-activated protein kinase kinase kinase kinase 40011
Serine/threonine-protein kinase LATS10011
Serine/threonine-protein kinase PAK 40011
Tyrosine-protein kinase ABL10011
Epidermal growth factor receptor0011
Sarcoplasmic/endoplasmic reticulum calcium ATPase 10101
High affinity nerve growth factor receptor0011
ADP/ATP translocase 20011
Protein kinase C beta type0011
Insulin receptor0011
Tyrosine-protein kinase Lck0011
Tyrosine-protein kinase Fyn0011
Cyclin-dependent kinase 10011
Eukaryotic translation initiation factor 4E0011
Glycogen phosphorylase, liver form0011
Tyrosine-protein kinase Fes/Fps0011
Adenine phosphoribosyltransferase0011
Tyrosine-protein kinase Yes0011
Tyrosine-protein kinase Lyn0011
Proto-oncogene tyrosine-protein kinase receptor Ret0011
Insulin-like growth factor 1 receptor0011
Signal recognition particle receptor subunit alpha0011
Cytochrome c1, heme protein, mitochondrial0011
Hepatocyte growth factor receptor0011
Tyrosine-protein kinase HCK0011
Platelet-derived growth factor receptor beta0011
Tyrosine-protein kinase Fgr0011
Serine/threonine-protein kinase A-Raf0011
Glycogen phosphorylase, brain form0011
Breakpoint cluster region protein0011
Serine/threonine-protein kinase pim-10011
Fibroblast growth factor receptor 10011
Cyclin-dependent kinase 40011
ADP/ATP translocase 30011
Proto-oncogene tyrosine-protein kinase Src0011
cAMP-dependent protein kinase type II-alpha regulatory subunit0011
Serine/threonine-protein kinase B-raf0011
Phosphorylase b kinase gamma catalytic chain, liver/testis isoform0011
Tyrosine-protein kinase Fer0011
Protein kinase C alpha type0011
cAMP-dependent protein kinase catalytic subunit alpha0011
General transcription and DNA repair factor IIH helicase subunit XPD0011
Casein kinase II subunit alpha'0011
Ras-related protein Rab-6A0011
Ephrin type-A receptor 10011
Multifunctional protein ADE20011
cAMP-dependent protein kinase catalytic subunit beta0011
Ferrochelatase, mitochondrial0011
Ribosomal protein S6 kinase beta-10011
Tyrosine-protein kinase JAK10011
Cyclin-dependent kinase 20011
Beta-adrenergic receptor kinase 10011
Probable ATP-dependent RNA helicase DDX60011
Peptidyl-prolyl cis-trans isomerase FKBP1A0101
MAP/microtubule affinity-regulating kinase 30011
Deoxycytidine kinase0011
Mitogen-activated protein kinase 10011
Ephrin type-A receptor 20011
Ephrin type-B receptor 20011
Non-receptor tyrosine-protein kinase TYK20011
UMP-CMP kinase 0011
Phosphatidylethanolamine-binding protein 10011
Wee1-like protein kinase0011
Heme oxygenase 20011
S-adenosylmethionine synthase isoform type-20011
DnaJ homolog subfamily A member 10011
RAC-alpha serine/threonine-protein kinase0011
RAC-beta serine/threonine-protein kinase0011
Dual specificity protein kinase TTK0011
DNA replication licensing factor MCM40011
Myosin-100011
Dual specificity mitogen-activated protein kinase kinase 20011
Receptor-type tyrosine-protein kinase FLT30011
Bone morphogenetic protein receptor type-1A0011
Activin receptor type-1B0011
TGF-beta receptor type-10011
Serine/threonine-protein kinase receptor R30011
TGF-beta receptor type-20011
Electron transfer flavoprotein subunit beta0011
Tyrosine-protein kinase CSK0011
Glycine--tRNA ligase0011
Protein kinase C iota type0011
Exosome RNA helicase MTR40011
Tyrosine-protein kinase Tec0011
Tyrosine-protein kinase ABL20011
Tyrosine-protein kinase FRK0011
G protein-coupled receptor kinase 60011
Tyrosine-protein kinase SYK0011
26S proteasome regulatory subunit 6B0011
Mitogen-activated protein kinase 80011
Mitogen-activated protein kinase 90011
Dual specificity mitogen-activated protein kinase kinase 30011
Phosphatidylinositol 5-phosphate 4-kinase type-2 alpha0011
Casein kinase I isoform alpha0011
Casein kinase I isoform delta0011
MAP kinase-activated protein kinase 20011
Elongation factor Tu, mitochondrial0011
Choline-phosphate cytidylyltransferase A0011
Cysteine--tRNA ligase, cytoplasmic0011
Casein kinase I isoform epsilon0011
Very long-chain specific acyl-CoA dehydrogenase, mitochondrial0011
Dual specificity protein kinase CLK10011
Dual specificity protein kinase CLK20011
Dual specificity protein kinase CLK30011
Glycogen synthase kinase-3 alpha0011
Glycogen synthase kinase-3 beta0011
Cyclin-dependent kinase 70011
Cyclin-dependent kinase 90011
Ras-related protein Rab-27A0011
Interleukin-1 receptor-associated kinase 10011
Ribosomal protein S6 kinase alpha-30011
Serine/threonine-protein kinase Nek20011
Serine/threonine-protein kinase Nek30011
Dual specificity mitogen-activated protein kinase kinase 60011
Serine/threonine-protein kinase PLK10011
LIM domain kinase 10011
LIM domain kinase 20011
Mitogen-activated protein kinase 100011
Tyrosine--tRNA ligase, cytoplasmic0011
Ephrin type-B receptor 30011
Ephrin type-A receptor 50011
Ephrin type-B receptor 40011
Ephrin type-A receptor 40011
Adenylate kinase 2, mitochondrial0011
Adenosine kinase0011
Ras-related protein Rab-100011
Actin-related protein 30011
Actin-related protein 20011
GTP-binding nuclear protein Ran0011
Peptidyl-prolyl cis-trans isomerase FKBP1A0426
Peptidyl-prolyl cis-trans isomerase FKBP1B0022
Casein kinase I isoform gamma-20011
Cyclin-dependent kinase 60011
Cyclin-dependent-like kinase 5 0011
Cyclin-dependent kinase 160011
Cyclin-dependent kinase 170011
ATP-dependent 6-phosphofructokinase, platelet type0011
Dual specificity mitogen-activated protein kinase kinase 10011
Protein kinase C theta type0011
Activin receptor type-10011
Macrophage-stimulating protein receptor0011
Focal adhesion kinase 10011
Protein kinase C zeta type0011
Protein kinase C delta type0011
Tyrosine-protein kinase BTK0011
Cyclin-dependent kinase 180011
Activated CDC42 kinase 10011
Epithelial discoidin domain-containing receptor 10011
Mitogen-activated protein kinase kinase kinase kinase 20011
Tyrosine-protein kinase Mer0011
Serine/threonine-protein kinase 40011
Dual specificity mitogen-activated protein kinase kinase 50011
Mitogen-activated protein kinase 70011
Serine/threonine-protein kinase PAK 20011
Serine/threonine-protein kinase 30011
Mitogen-activated protein kinase kinase kinase 10011
Integrin-linked protein kinase0011
Peptidyl-prolyl cis-trans isomerase FKBP50202
Rho-associated protein kinase 10011
Non-receptor tyrosine-protein kinase TNK10011
Calcium/calmodulin-dependent protein kinase type II subunit gamma0011
Calcium/calmodulin-dependent protein kinase type II subunit delta0011
Dual specificity tyrosine-phosphorylation-regulated kinase 1A0011
Activin receptor type-2B0011
Bone morphogenetic protein receptor type-20011
Protein-tyrosine kinase 60011
cGMP-dependent protein kinase 1 0011
Cyclin-dependent kinase 130011
Inhibitor of nuclear factor kappa-B kinase subunit epsilon0011
Protein-tyrosine kinase 2-beta0011
Maternal embryonic leucine zipper kinase0011
Structural maintenance of chromosomes protein 1A0011
Chromodomain-helicase-DNA-binding protein 40011
Peroxisomal acyl-coenzyme A oxidase 10011
Delta(24)-sterol reductase0011
Ribosomal protein S6 kinase alpha-10011
Dual specificity testis-specific protein kinase 10011
Myosin light chain kinase, smooth muscle0011
Mitogen-activated protein kinase 110011
Serine/threonine-protein kinase STK110011
Serine/threonine-protein kinase N10011
Serine/threonine-protein kinase N20011
Mitogen-activated protein kinase 140011
Calcium/calmodulin-dependent protein kinase type IV0011
Mitogen-activated protein kinase kinase kinase 110011
AP2-associated protein kinase 10011
Myosin light chain kinase 30011
Uncharacterized aarF domain-containing protein kinase 50011
Programmed cell death protein 40011
Putative heat shock protein HSP 90-beta 20011
Serine/threonine-protein kinase MRCK alpha0011
Serine/threonine-protein kinase MRCK gamma0011
Acyl-CoA dehydrogenase family member 100011
Serine/threonine-protein kinase N30011
Serine/threonine-protein kinase ULK30011
Uncharacterized protein FLJ452520011
Acyl-CoA dehydrogenase family member 110011
Serine/threonine-protein kinase/endoribonuclease IRE20011
Serine/threonine-protein kinase MARK20011
ATP-dependent RNA helicase DHX300011
Serine/threonine-protein kinase TAO10011
STE20-related kinase adapter protein alpha0011
Myosin-140011
AarF domain-containing protein kinase 10011
Mitogen-activated protein kinase kinase kinase kinase 30011
MAP kinase-activated protein kinase 50011
Regulatory-associated protein of mTOR0101
Misshapen-like kinase 10011
Atypical kinase COQ8A, mitochondrial0011
Phosphatidylinositol 5-phosphate 4-kinase type-2 gamma0011
Mitogen-activated protein kinase 150011
Serine/threonine-protein kinase Nek90011
ATP-dependent RNA helicase DDX10011
Mitogen-activated protein kinase kinase kinase kinase 10011
Aurora kinase B0011
MAP/microtubule affinity-regulating kinase 40011
Calcium/calmodulin-dependent protein kinase type 1G0011
Serine/threonine-protein kinase Nek10011
PAS domain-containing serine/threonine-protein kinase0011
Calcium/calmodulin-dependent protein kinase kinase 20011
EKC/KEOPS complex subunit TP53RK0011
Dual specificity testis-specific protein kinase 20011
Membrane-associated tyrosine- and threonine-specific cdc2-inhibitory kinase0011
Mitogen-activated protein kinase kinase kinase 50011
Mitogen-activated protein kinase kinase kinase 30011
Eukaryotic translation initiation factor 2-alpha kinase 10011
Target of rapamycin complex subunit LST80101
Nucleolar GTP-binding protein 10011
Serine/threonine-protein kinase D20011
RNA cytidine acetyltransferase0011
Serine/threonine-protein kinase SIK20011
STE20-like serine/threonine-protein kinase 0011
Serine/threonine-protein kinase TAO30011
dCTP pyrophosphatase 10011
Dual specificity protein kinase CLK40011
Casein kinase I isoform gamma-10011
Serine/threonine-protein kinase mTOR 0101
Phenylalanine--tRNA ligase beta subunit0011
Isoleucine--tRNA ligase, mitochondrial0011
BMP-2-inducible protein kinase0011
Obg-like ATPase 10011
Midasin0011
Interleukin-1 receptor-associated kinase 40011
Mitogen-activated protein kinase kinase kinase 200011
Cyclin-dependent kinase 120011
Serine/threonine-protein kinase 260011
Succinate--CoA ligase [ADP-forming] subunit beta, mitochondrial0011
Serine/threonine-protein kinase NLK0011
Serine/threonine-protein kinase TBK10011
Septin-90011
Ribosomal protein S6 kinase alpha-60011
TRAF2 and NCK-interacting protein kinase0011
Serine/threonine-protein kinase TAO20011
Broad substrate specificity ATP-binding cassette transporter ABCG20202
Serine/threonine-protein kinase ICK0011
RAC-gamma serine/threonine-protein kinase0011
Serine/threonine-protein kinase SIK30011
Mitogen-activated protein kinase kinase kinase 20011
Thyroid hormone receptor-associated protein 30011
Dual specificity tyrosine-phosphorylation-regulated kinase 1B0011
Mitogen-activated protein kinase kinase kinase kinase 50011
Receptor-interacting serine/threonine-protein kinase 30011
Serine/threonine-protein kinase MRCK beta0011
Interleukin-1 receptor-associated kinase 30011
Serine/threonine-protein kinase 240011
Casein kinase I isoform gamma-30011
Mitogen-activated protein kinase kinase kinase 40011
Carbonic anhydrase 0101
Chain A, Acetylcholinesterase0011
Chain A, Acetylcholinesterase0011
Chain A, Acetylcholinesterase0011
Chain A, Acetylcholinesterase0011
Chain A, Acetylcholinesterase0011
Chain A, Acetylcholinesterase0011
Chain A, Acetylcholinesterase0011
Acetylcholinesterase0101
Cytochrome P450 3A50101
Serine/threonine-protein phosphatase 2B catalytic subunit alpha isoform0101
Splicing factor 3B subunit 30101
Potassium channel subfamily K member 30101
cGMP-gated cation channel alpha-10011
Sodium channel protein type 7 subunit alpha0101
Sodium channel protein type 9 subunit alpha0202
Sodium channel protein type 2 subunit alpha0101
Sodium channel protein type 3 subunit alpha0101
Sodium channel protein type 8 subunit alpha0101
90-kda heat shock protein beta HSP90 beta, partial0101
estrogen receptor beta isoform 10101
heat shock protein HSP 90-alpha isoform 20101
tyrosine-protein phosphatase non-receptor type 7 isoform 20101
Dihydroxyacetone phosphate acyltransferase0001
30S ribosomal protein S60101
30S ribosomal protein S70101
50S ribosomal protein L150101
Tetracycline resistance protein, class B0001
72 kDa type IV collagenase0101
50S ribosomal protein L100101
50S ribosomal protein L110101
50S ribosomal protein L7/L120101
50S ribosomal protein L190101
50S ribosomal protein L10101
50S ribosomal protein L200101
50S ribosomal protein L270101
50S ribosomal protein L280101
50S ribosomal protein L290101
50S ribosomal protein L310101
50S ribosomal protein L31 type B0101
50S ribosomal protein L320101
50S ribosomal protein L330101
50S ribosomal protein L340101
50S ribosomal protein L350101
50S ribosomal protein L360101
30S ribosomal protein S100101
30S ribosomal protein S110101
30S ribosomal protein S120101
30S ribosomal protein S130101
30S ribosomal protein S160101
30S ribosomal protein S180101
30S ribosomal protein S190101
30S ribosomal protein S200101
30S ribosomal protein S20101
30S ribosomal protein S30101
30S ribosomal protein S40101
30S ribosomal protein S50101
30S ribosomal protein S80101
30S ribosomal protein S90101
50S ribosomal protein L130101
50S ribosomal protein L140101
50S ribosomal protein L160101
50S ribosomal protein L230101
30S ribosomal protein S150101
Multidrug transporter MdfA0101
50S ribosomal protein L170101
50S ribosomal protein L210101
50S ribosomal protein L300101
50S ribosomal protein L60101
30S ribosomal protein S140101
30S ribosomal protein S170101
30S ribosomal protein S10101
50S ribosomal protein L180101
Neutrophil collagenase0101
Collagenase 30101
Cannabinoid receptor 10101
50S ribosomal protein L20101
50S ribosomal protein L30101
50S ribosomal protein L240101
50S ribosomal protein L40101
50S ribosomal protein L220101
50S ribosomal protein L50101
30S ribosomal protein S210101
50S ribosomal protein L250101
50S ribosomal protein L36 20101
P2Y purinoceptor 120101
Protein-arginine deiminase type-40101
Solute carrier family 22 member 70001
Cereblon isoform 40202
cAMP-specific 3',5'-cyclic phosphodiesterase 4A0101
Prostaglandin G/H synthase 20101
cAMP-specific 3',5'-cyclic phosphodiesterase 4B0101
cAMP-specific 3',5'-cyclic phosphodiesterase 4C0101
cAMP-specific 3',5'-cyclic phosphodiesterase 4D0101
DNA-binding protein Ikaros0001
DNA damage-binding protein 10112
Protein cereblon0214
Chain A, CHORISMATE MUTASE0101
Chain A, TYROSYL-tRNA SYNTHETASE0011
Plasma kallikrein0001
Adenosine receptor A10001
Adenosine receptor A2a0001
Carbonic anhydrase0001
Glutamate receptor ionotropic, NMDA 2A 0001
Glutamate receptor ionotropic, NMDA 2B0001
Glutamate receptor ionotropic, NMDA 2C0001
SLC16A10 protein0001
Carbonic anhydrase 0001
Carbonic anhydrase-like protein, putative0001
Carbonic anhydrase0001
Carbonic anhydrase0001
Glutamate receptor ionotropic, NMDA 2D0001
Carbonic anhydrase 0001
Tubulin--tyrosine ligase0101
Glutamate receptor ionotropic, NMDA 3B0001
Monocarboxylate transporter 100001
Taste receptor type 2 member 140001
Glutamate receptor ionotropic, NMDA 3A0001
Cocaine esterase0101
Cytochrome P450 2A60101
Aldo-keto reductase family 1 member A10101
Aldo-keto reductase family 1 member A10101
Aldo-keto reductase family 1 member A10101
Aldo-keto reductase family 1 member B70101
NAD-dependent protein deacylase sirtuin-5, mitochondrial0101
[prepared from compound, protein, and bioassay information from National Library of Medicine (NLM), extracted Dec-2023]