A 2-oxo monocarboxylic acid that is valeric acid carrying oxo- and methyl substituents at C-2 and C-3, respectively. An alpha-keto acid analogue and metabolite of isoleucine in man, animals and bacteria. Used as a clinical marker for maple syrup urine disease (MSUD).
ChEBI ID: 35932
There are 2 compounds belonging to this class, involving 0 studies.
Member | Definition | Role |
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(S)-3-methyl-2-oxovaleric-acid | The (S)-enantiomer of 3-methyl-2-oxovaleric acid. | |
(R)-3-methyl-2-oxovaleric-acid | The (R)-enantiomer of 3-methyl-2-oxovaleric acid. |
Pre-1990 | 1990-2000 | 2001-2010 | 2011-2020 | Post-2020 |
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